Carnitine: Metabolism and clinical chemistry

Carnitine--metabolism and functions

1983 • 1,620 citations

Mitochondrial myopathies

1985 • 682 citations

CARNITINE

1988 • 610 citations

Carnitine Deficiency of Human Skeletal Muscle with Associated Lipid Storage Myopathy: A New Syndrome

1973 • 506 citations

Mechanism of activation of pyruvate dehydrogenase by dichloroacetate and other halogenated carboxylic acids

1974 • 492 citations

Muscle Carnitine Palmityltransferase Deficiency and Myoglobinuria

1973 • 476 citations

Intracellular Protein Catabolism and its Control During Nutrient Deprivation and Supply

1987 • 437 citations

Regulation of pyruvate dehydrogenase in rat heart. Mechanism of regulation of proportions of dephosphorylated and phosphorylated enzyme by oxidation of fatty acids and ketone bodies and of effects of diabetes: role of coenzyme A, acetyl-coenzyme A and reduced and oxidized nicotinamide-adenine dinucleotide

1976 • 399 citations

The syndrome of systemic carnitine deficiency

1975 • 397 citations

Reversible Inhibition of Mitochondrial Adenosine Diphosphate Phosphorylation by Long Chain Acyl Coenzyme A Esters

1971 • 357 citations

Changes in tissue levels of carnitine and other metabolites during myocardial ischemia and anoxia

1978 • 249 citations

Carnitine Metabolism and Function in Humans

1986 • 249 citations

Tissue distribution of carnitine biosynthetic enzymes in man

1980 • 228 citations

Carnitine

1983 • 188 citations

Increases in walking distance in patients with peripheral vascular disease treated with L-carnitine: a double-blind, cross-over study.

1988 • 173 citations

Carnitine metabolism and inborn errors

1984 • 139 citations

Protein Methylation: Chemical, Enzymological, and Biological Significance

1975 • 120 citations

Valproylcarnitine: a novel drug metabolite identified by fast atom bombardment and thermospray liquid chromatography-mass spectrometry

1985 • 117 citations

Carnitine Biosynthesis, Metabolism, and Functions

1980 • 115 citations

Role of Carnitine in Human Nutrition

1988 • 115 citations

The interaction of long-chain acyl CoA with membranes

1983 • 107 citations

Quantitation of the efflux of acylcarnitines from rat heart, brain, and liver mitochondria.

1986 • 102 citations

The biochemical basis of mitochondrial diseases

1988 • 95 citations

High doses of L-carnitine in acute myocardial infarction: metabolic and antiarrhythmic effects

1989 • 86 citations

Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl-CoA/CoA ratios by <scp>l</scp>-carnitine in vivo

1983 • 76 citations

Stimulation of oxidation of mitochondrial fatty acids and of acetate by acetylcarnitine

1965 • 69 citations

Tissue specific depletion of L-carnitine in rat heart and skeletal muscle by D-carnitine

1981 • 64 citations

Clinical varieties of carnitine and carnitine palmitoyltransferase deficiency

1987 • 51 citations

DL-aminocarnitine and acetyl-DL-aminocarnitine. Potent inhibitors of carnitine acyltransferases and hepatic triglyceride catabolism.

1985 • 45 citations

Carnitine and glucuronic acid conjugates of pivalic acid

1985 • 42 citations

[28] Short-chain acylcarnitines: Identification and quantitation

1986 • 41 citations

Sites and regulation of carnitine biosynthesis in mammals.

1982 • 39 citations

Stabilising action of carnitine on energy linked processes in rat liver mitochondria

1985 • 31 citations

The role of carnitine in the conjugation of acidic xenobiotics.

1986 • 29 citations

γ-butyrobetaine in tissues and serum of fed and starved rats determined by an enzymic radioisotopic procedure

1984 • 25 citations

Isovalerylcarnitine is a specific activator of calpain of human neutrophils

1987 • 23 citations

An enzymatic method for the determination of butyrobetaine via conversion to carnitine after isolation by high performance liquid chromatography

1988 • 21 citations

Carnitine transport in rat heart slices: I. The action of thiol reagents on the acetylcarnitine/carnitine exchange.

1985 • 20 citations

Lipid metabolism in the normoxic and ischaemic heart

1987 • 17 citations

Myocardial carnitine transport

1987 • 17 citations

Carnitine transport in rat heart slices: II. The carnitine/deoxycarnitine antiport.

1985 • 16 citations

Involvement of long-chain acyl CoA in the antagonistic effects of halothane and L-carnitine on mitochondrial energy-linked processes

1986 • 14 citations

l-Carnitine effect on halothane-treated mitochondria

1986 • 14 citations

On the transport mechanisms of carnitine and its derivative in rat heart slices.

1982 • 12 citations