Relationship between ataxin-1 nuclear inclusions and Purkinje cell specific proteins in SCA-1 transgenic mice

Glutamate neurotoxicity and diseases of the nervous system

1988 • 7,257 citations

Calbindin D-28k and parvalbumin in the rat nervous system

1990 • 2,068 citations

Expansion of an unstable trinucleotide CAG repeat in spinocerebellar ataxia type 1

1993 • 1,596 citations

Calcium-binding proteins in the nervous system

1992 • 1,321 citations

Glutamine repeats as polar zippers: their possible role in inherited neurodegenerative diseases.

1994 • 1,065 citations

Excitotoxity and the NMDA receptor

1987 • 1,053 citations

Ataxin-1 Nuclear Localization and Aggregation

1998 • 959 citations

Intranuclear Inclusions of Expanded Polyglutamine Protein in Spinocerebellar Ataxia Type 3

1997 • 821 citations

Huntingtin is a cytoplasmic protein associated with vesicles in human and rat brain neurons

1995 • 736 citations

Short protocols in molecular biology

1990 • 720 citations

SCA1 transgenic mice: A model for neurodegeneration caused by an expanded CAG trinucleotide repeat

1995 • 582 citations

Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

1997 • 528 citations

Evidence for calcium-reducing and excitoprotective roles for the calcium-binding protein calbindin-1328k in cultured hippocampal neurons

1991 • 518 citations

Widespread expression of Huntington's disease gene (IT15) protein product

1995 • 516 citations

Changes in Ca2+-binding proteins in human neurodegenerative disorders

1992 • 413 citations

Parvalbumin-immunoreactive neurons in the rat neostriatum: a light and electron microscopic study

1990 • 408 citations

Ataxia and altered dendritic calcium signaling in mice carrying a targeted null mutation of the calbindin D28k gene

1997 • 397 citations

Intranuclear Neuronal Inclusions: A Common Pathogenic Mechanism for Glutamine-Repeat Neurodegenerative Diseases?

1997 • 392 citations

Identification and characterization of the gene causing type 1 spinocerebellar ataxia

1994 • 369 citations

HIP-I: A huntingtin interacting protein isolated by the yeast two-hybrid system

1997 • 335 citations

Identification and localization of huntingtin in brain and human lymphoblastoid cell lines with anti-fusion protein antibodies.

1995 • 299 citations

Expression analysis of the ataxin–1 protein in tissues from normal and spinocerebellar ataxia type 1 individuals

1995 • 294 citations

Antigenic changes similar to those seen in neurofibrillary tangles are elicited by glutamate and Ca2+ influx in cultured hippocampal neurons

1990 • 283 citations

Purkinje Cell Expression of a Mutant Allele ofSCA1in Transgenic Mice Leads to Disparate Effects on Motor Behaviors, Followed by a Progressive Cerebellar Dysfunction and Histological Alterations

1997 • 270 citations

The cerebellar leucine-rich acidic nuclear protein interacts with ataxin-1

1997 • 249 citations

Mice Lacking Ataxin-1 Display Learning Deficits and Decreased Hippocampal Paired-Pulse Facilitation

1998 • 204 citations

Diffusion Across the Nuclear Envelope Inhibited by Depletion of the Nuclear Ca ²⁺ Store

1995 • 192 citations

Neuronal death in vitro: parallelism between survivability of hippocampal neurones and sustained elevation of cytosolic Ca2+ after exposure to glutamate receptor agonist

1988 • 178 citations

Chemical composition, affinity for calcium, and related properties of the vitamin D dependent calcium-binding protein

1974 • 176 citations

Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions?

1998 • 163 citations

Spinocerebellar ataxia type-1 and spinobulbar muscular atrophy gene products interact with glyceraldehyde-3-phosphate dehydrogenase

1996 • 148 citations

Huntingtin-associated protein 1 (HAP1) binds to a Trio-like polypeptide, with a rac1 guanine nucleotide exchange factor domain

1997 • 129 citations

Purkinje cell protein-2 regulatory regions and transgene expression in cerebellar compartments.

1991 • 124 citations

Expression of calbindin-D28K in motoneuron hybrid cells after retroviral infection with calbindin-D28K cDNA prevents amyotrophic lateral sclerosis IgG-mediated cytotoxicity.

1996 • 91 citations

Distribution of Calretinin, Calbindin D28k, and Parvalbumin in Subcellular Fractions of Rat Cerebellum: Effects of Calcium

1995 • 81 citations

Reduced immunoreactivity to calcium-binding proteins in Purkinje cells precedes onset of ataxia in spinocerebellar ataxia-1 transgenic mice

1998 • 69 citations

Parvalbumin in the monkey striate cortex: a quantitative immunoelectron-microscopy study

1991 • 57 citations

Calbindin-D28k in nerve cell nuclei

1997 • 50 citations

Ca²⁺ Handling Systems and Neuronal Aging^a

1989 • 34 citations

Decreased parvalbumin immunoreactivity in surviving Purkinje cells of patients with spinocerebellar ataxia-1

1996 • 31 citations

Morphometric Studies in Dominant Olivopontocerebellar Atrophy

1990 • 27 citations

Purification, calcium-binding properties, and conformational studies on a 28-kDa cholecalcin-like protein from bovine brain.

1985 • 18 citations