Heterologous expression of delta F508 CFTR results in decreased sialylation of membrane glycoconjugates

Identification of the Cystic Fibrosis Gene: Cloning and Characterization of Complementary DNA

1989 • 7,327 citations

ACIDIFICATION OF THE ENDOCYTIC AND EXOCYTIC PATHWAYS

1986 • 1,977 citations

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

1992 • 1,230 citations

Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)

1992 • 937 citations

Cystic fibrosis: molecular biology and therapeutic implications

1992 • 820 citations

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

1990 • 706 citations

Generation of cAMP-Activated Chloride Currents by Expression of CFTR

1991 • 550 citations

Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

1991 • 498 citations

Defective acidification of intracellular organelles in cystic fibrosis

1991 • 490 citations

Regulation of Plasma Membrane Recycling by CFTR

1992 • 339 citations

Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis.

1989 • 216 citations

Abnormal localization of cystic fibrosis transmembrane conductance regulator in primary cultures of cystic fibrosis airway epithelia.

1992 • 171 citations

Mechanism of cholera toxin action on a polarized human intestinal epithelial cell line: role of vesicular traffic

1992 • 150 citations

Protein kinase A regulates chloride conductance in endocytic vesicles from proximal tubule

1990 • 136 citations

Thyrotropin induces the acidification of the secretory granules of parafollicular cells by increasing the chloride conductance of the granular membrane.

1988 • 94 citations

Glycoprotein synthesis, transport, and secretion by epithelial cells of human rectal mucosa: normal and cystic fibrosis.

1977 • 88 citations

Human Intestinal Mucin in Cystic Fibrosis

1983 • 85 citations

Interaction of cholera toxin with rat intestinal brush border membranes. Relative roles of gangliosides and galactoproteins as toxin receptors.

1981 • 75 citations

Respiratory mucous secretions in patients with cystic fibrosis: relationship between levels of highly sulfated mucin component and severity of the disease

1983 • 63 citations

Altered Fucosylation of Membrane Glycoproteins from Cystic Fibrosis Fibroblasts1

1985 • 41 citations

Differential binding kinetics of cholera toxin to intestinal microvillus membrane during development

1987 • 34 citations

Additional fucosyl residues on membrane glycoproteins but not a secreted glycoprotein from cystic fibrosis fibroblasts

1990 • 31 citations

Les glycopeptides du mucus bronchique fibrillaire dans la mucoviscidose

1972 • 21 citations