Orotic Acid in Urine and Hyperammonemia

Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia.

1979 • 210 citations

Interrelationships between gluconeogenesis and ureogenesis in isolated hepatocytes.

1978 • 129 citations

Control of Pyrimidine Biosynthesis in Mammalian Tissues

1969 • 129 citations

Aggregation states and catalytic properties of the multienzyme complex catalyzing the initial steps of pyrimidine biosynthesis in rat liver

1975 • 106 citations

Enzymatic synthesis of acetylglutamate by mammalian liver preparations and its stimulation by arginine

1971 • 95 citations

Diagnostic value of orotic acid excretion in heritable disorders of the urea cycle and in hyperammonemia due to organic acidurias

1980 • 93 citations

Orotic acid biosynthesis in rat liver: Studies on the source of carbamoylphosphate

1977 • 82 citations

Failure of the Normal Ureagenic Response to Amino Acids in Organic Acid-loaded Rats

1980 • 67 citations

On the availability of intramitochondrial carbamoylphosphate for the extramitochondrial biosynthesis of pyrimidines

1969 • 54 citations

Determination of Orotic and Dihydroorotic Acids in Biological Fluids and Tissues

1975 • 40 citations

A Case of Carbamyl Phosphate Synthetase Deficiency

1972 • 35 citations

Urinary purines and pyrimidines in patients with hyperammonemia of various origins

1980 • 34 citations

Effect of propionate and pyruvate on citrulline synthesis and ATP content in rat liver mitochondria

1979 • 33 citations

Orotic acid biosynthesis in arginine-deficient rats

1979 • 24 citations

HEREDITARY ORNITHINE TRANSCARBAMYLASE DEFICIENCY

1975 • 24 citations

Purine and pyrimidine metabolism in hereditary orotic aciduria: some unexpected effects of allopurinol

1980 • 20 citations

Effect of Ammonium Ion on Pyrimidine Synthesis de novo in Isolated Rat Hepatocytes

1981 • 13 citations

Haptoglobin types and subtypes in Alzheimer's disease and senile dementia

1973 • 10 citations

Hepatic Ornithine Aminotransferase in the Rat after Portacaval Shunt

1980 • 1 citations

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