Failure of the Normal Ureagenic Response to Amino Acids in Organic Acid-loaded Rats

Adaptive Characteristics of Urea Cycle Enzymes in the Rat

1962 • 738 citations

Amino Acid Diets and Maximal Growth in the Rat

1965 • 498 citations

Effect of glucagon on metabolite compartmentation in isolated rat liver cells during gluconeogenesis from lactate

1977 • 234 citations

Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia.

1979 • 210 citations

CATALYTIC RÔLE OF GLUTAMATE DERIVATIVES IN CITRULLINE BIOSYNTHESIS

1953 • 185 citations

Role of Acetylglutamate in Ureotelism

1971 • 160 citations

Propionicacidemia, a New Inborn Error of Metabolism

1968 • 160 citations

Pyruvate Carboxylase

1967 • 144 citations

Short term regulation of ureagenesis.

1980 • 125 citations

Role of Acetylglutamate in Ureotelism

1978 • 100 citations

N‐Acetylglutamate Synthetase from Rat‐Liver Mitochondria

1978 • 100 citations

Enzymatic synthesis of acetylglutamate by mammalian liver preparations and its stimulation by arginine

1971 • 95 citations

The effect of acute and prolonged ethanol treatment on the concentrations of coenzyme A, carnitine and their derivatives in rat liver

1973 • 83 citations

The inhibition by methylmalonic acid of malate transport by the dicarboxylate carrier in rat liver mitochondria

1971 • 70 citations

Effect of ornithine and lactate on urea synthesis in isolated hepatocytes

1976 • 55 citations

Effect of Propionic Acid on Fatty Acid Oxidation and Ureagenesis

1976 • 54 citations

Adaptive changes in the capacity of systems used for the synthesis of citrulline in rat liver mitochondria in response to high- and low-protein diets

1974 • 48 citations

Effects of branched chain alpha-ketoacids on the metabolism of isolated rat liver cells. II. Interactions with gluconeogenesis and urea synthesis.

1979 • 46 citations

Correlation between serum propionate and blood ammonia concentrations in propionic acidemia

1978 • 39 citations

Effect of pent-4-enoic acid, propionic acid and other short-chain fatty acids on citrulline synthesis in rat liver mitochondria

1976 • 38 citations

Effect of propionate and pyruvate on citrulline synthesis and ATP content in rat liver mitochondria

1979 • 33 citations

Analysis of Regulatory Factors for Urea Synthesis by Isolated Perfused Rat Liver

1975 • 31 citations

INTERPRETATION OF THE DEHYDRATION OF ACETYLGLUTAMIC ACID BY MEANS OF GLUTAMYLTHIOHYDANTOIN DERIVATIVES

1930 • 24 citations

Propionate and succinate effects on acetyl glutamate biosynthesis by rat liver mitochondria

1979 • 17 citations

L-(-)-Malat Bestimmung mit Malat-Dehydrogenase und NAD

1970 • 17 citations

Inhibition of mitochondrial carbamyl phosphate synthetase in rat and human liver by ACYL CoA esters : a possible mechanism for hyperammonemia in the inherited organic acidemias

1981 • 5 citations

Ketoglutarat UV-spektrophotometrische Bestimmung

1970 • 2 citations

Bestimmung mit Hexokinase und Glucose-6-phosphat Dehydrogenase

1970 • 1 citations