Natural history of liver disease in cystic fibrosis

Long-Term Study of One Hundred Five Patients with Cystic Fibrosis

1958 • 1,014 citations

One-Second Needle Biopsy of the Liver

1958 • 386 citations

Vitamin A Transport in Human Vitamin A Toxicity

1976 • 325 citations

Stimulation of collagen α1(I) gene expression is associated with lipid peroxidation in hepatocellular injury: A link to tissue fibrosis?

1994 • 249 citations

Prevalence of liver disease in cystic fibrosis.

1991 • 224 citations

Analysis of risk factors for the development of liver disease associated with cystic fibrosis

1994 • 194 citations

Liver Disease and Common-Bile-Duct Stenosis in Cystic Fibrosis

1988 • 185 citations

A two-year prospective study of the effect of ursodeoxycholic acid on urinary bile acid excretion and liver morphology in cystic fibrosis-associated liver disease

1998 • 171 citations

Severity of cystic fibrosis in patients homozygous and heterozygous for ΔF508 mutation

1991 • 167 citations

Hepatic changes in young infants with cystic fibrosis: Possible relation to focal biliary cirrhosis

1975 • 153 citations

A distinctive type of biliary cirrhosis of the liver associated with cystic fibrosis of the pancreas; recognition through signs of portal hypertension.

1956 • 151 citations

Liver cirrhosis in cystic fibrosis--therapeutic implications and long term follow up.

1993 • 140 citations

A DISTINCTIVE TYPE OF BILIARY CIRRHOSIS OF THE LIVER ASSOCIATED WITH CYSTIC FIBROSIS OF THE PANCREAS

1956 • 137 citations

Determination of the Hepatic Galactose Elimination Capacity after a Single Intravenous Injection in Man: The reproducibility and the influence of uneven distribution

1963 • 126 citations

A simple method for determination of antipyrine clearance

1982 • 125 citations

NO CHILDHOOD

1975 • 125 citations

Oxygen free radicals and antioxidants in cystic fibrosis: the concept of an oxidant‐antioxidant imbalance

1994 • 104 citations

Liver transplantation for hepatic cirrhosis in cystic fibrosis.

1996 • 100 citations

Apparent Potentiation of Acetaminophen Hepatotoxicity by Alcohol

1980 • 90 citations

Intestinal bile acid malabsorption in cystic fibrosis.

1993 • 90 citations

Home intravenous antibiotic treatment of patients with cystic fibrosis

1992 • 88 citations

Amoxicillin-clavulanate potassium-associated cholestasis

1989 • 87 citations

Altered antioxidant status and increased lipid peroxidation in children with cystic fibrosis

1995 • 87 citations

The Pathological Changes in the Liver in Cystic Fibrosis of the Pancreas

1957 • 86 citations

Genotype analysis for ΔF508, G551D and R553X mutations in children and young adults with cystic fibrosis with and without chronic liver disease

1992 • 85 citations

Symptomatic Hepatic Disease In Cystic Fibrosis: Incidence, Course, And Outcome Of Portal Systemic Shunting

1976 • 83 citations

Biliary complications of cystic fibrosis.

1992 • 78 citations

Liver transplantation for hepatic cirrhosis in cystic fibrosis.

1994 • 77 citations

Can the Histologic Changes of Cystic Fibrosis-Associated Hepatobiliary Disease be Predicted by Clinical Criteria?

1997 • 71 citations

Morphological findings in the liver of children with cystic fibrosis: A light and electron microscopical study

1986 • 67 citations

Essential fatty acid deficiency and predisposition to lung disease in cystic fibrosis

1996 • 59 citations

HEPATIC COMPLICATIONS OF CYSTIC FIBROSIS

1981 • 56 citations

Meconium Ileus and Its Equivalent as a Risk Factor for the Development of Cirrhosis

1989 • 53 citations

Liver function and morphology during long‐term fatty acid supplementation in cystic fibrosis

1994 • 49 citations

Trimethoprim-Sulfamethoxazole-Induced Intrahepatic Cholestasis

1980 • 44 citations

Pseudomonas aeruginosa Exotoxin in Mice: Histopathology and Serum Enzyme Changes

1976 • 44 citations

Hepatic Drug Metabolism in Cystic Fibrosis: Recent Developments and Future Directions

1993 • 36 citations

Prospective Study of Fatty Acid Supplementation Over 3 Years in Patients with Cystic Fibrosis

1983 • 36 citations

Meconium Ileus and Its Equivalent as a Risk Factor for the Development of Cirrhosis

1989 • 33 citations

Vitamin A Concentration in the Liver Decreases with Age in Patients with Cystic Fibrosis

1997 • 30 citations

Deletion ΔF508 and clinical expression of cystic fibrosis‐related liver disease

1992 • 25 citations

Imipenem/cilastatin, an alternative treatment of pseudomonas infection in cystic fibrosis

1988 • 24 citations

Antibiotic therapy of pulmonary infections in cystic fibrosis. Dosage schedules and duration of treatment.

1988 • 23 citations

Cloxacillin-induced cholestatic jaundice.

1986 • 23 citations

Role of vitamin A in liver fibrosis

1995 • 23 citations

Urinary Bile Acid Excretion in Correlation to Liver Histopathology in Cystic Fibrosis

1980 • 21 citations

Comparison of efficacy and tolerance of intravenously and orally administered ciprofloxacin in cystic fibrosis patients with acute exacerbations of lung infection.

1989 • 19 citations

Fasting Serum Bile Acid Levels in Relation to Liver Histopathology in Cystic Fibrosis

1985 • 18 citations

Prognosis in cystic fibrosis.

1973 • 18 citations

Serum Enzymes and Enzyme Profiles in the Diagnosis of Liver and Biliary Tract Disease

1985 • 8 citations

High doses of aminoglycosides did not produce liver toxicity in patients with cystic fibrosis

1994 • 5 citations