Heterozygosity for a Surfactant Protein C Gene Mutation Associated with Usual Interstitial Pneumonitis and Cellular Nonspecific Interstitial Pneumonitis in One Kindred

Idiopathic Pulmonary Fibrosis: Diagnosis and Treatment

2000 • 2,535 citations

Idiopathic Pulmonary Fibrosis: Prevailing and Evolving Hypotheses about Its Pathogenesis and Implications for Therapy

2001 • 1,727 citations

Idiopathic Pulmonary Fibrosis

1998 • 1,255 citations

The mechanism of Z α1-antitrypsin accumulation in the liver

1992 • 1,030 citations

A Mutation in the Surfactant Protein C Gene Associated with Familial Interstitial Lung Disease

2001 • 888 citations

The VITESSE algorithm for rapid exact multilocus linkage analysis via genotype set–recoding and fuzzy inheritance

1995 • 514 citations

Morphological and biochemical characterization and analysis of apoptosis

1997 • 478 citations

Pulmonary surfactant in health and human lung diseases: state of the art

1999 • 474 citations

Function of Surfactant Proteins B and C

2001 • 364 citations

Altered stability of pulmonary surfactant in SP-C-deficient mice

2001 • 282 citations

Adult familial cryptogenic fibrosing alveolitis in the United Kingdom

2000 • 229 citations

Mutations in the Surfactant Protein C Gene Associated With Interstitial Lung Disease

2002 • 192 citations

Increased Risk of Fibrosing Alveolitis Associated with Interleukin-1 Receptor Antagonist and Tumor Necrosis Factor- α Gene Polymorphisms

2000 • 186 citations

Alterations in the alveolar epithelium after injury leading to pulmonary fibrosis.

1996 • 175 citations

Familial Idiopathic Pulmonary Fibrosis

1986 • 172 citations

Surfactant protein deficiency in familial interstitial lung disease

2001 • 147 citations

Folding of Secretory and Membrane Proteins

1998 • 143 citations

Molecular and phenotypic variability in the congenital alveolar proteinosis syndrome associated with inherited surfactant protein B deficiency

1994 • 134 citations

The pathogenesis of pulmonary fibrosis: Is there a fibrosis gene?

1997 • 116 citations

Lamellar Body Formation in Normal and Surfactant Protein B-Deficient Fetal Mice

2000 • 116 citations

α1-ANTITRYPSIN PHENOTYPES IN FIBROSING ALVEOLITIS AND RHEUMATOID ARTHRITIS

1977 • 109 citations

Biosynthesis of surfactant protein C: characterization of aggresome formation by EGFP chimeras containing propeptide mutants lacking conserved cysteine residues

2001 • 84 citations

FAMILIAL FIBROCYSTIC PULMONARY DYSPLASIA AND ITS RELATION TO THE HAMMAN-RICH SYNDROME

1959 • 81 citations

Desquamative Interstitial Pneumonitis in Children

1980 • 68 citations

Structure and functions of a dimeric form of surfactant protein SP-C: a Fourier transform infrared and surfactometry study

1992 • 64 citations

Familial Hamman-Rich Syndrome

1969 • 61 citations

Synthetic Processing of Surfactant Protein C by Alevolar Epithelial Cells

1998 • 57 citations

Absence of Lamellar Bodies with Accumulation of Dense Bodies Characterizes a Novel Form of Congenital Surfactant Defect

2000 • 57 citations

Genetic Studies in Familial Fibrosing Alveolitis

1986 • 53 citations

Alveolar type II cell apoptosis

2001 • 48 citations

Familial chronic interstitial pneumonia.

1973 • 47 citations

Increased D allele frequency of the angiotensin-converting enzyme gene in pulmonary fibrosis

2001 • 44 citations

The C-terminal Domain of the Pulmonary Surfactant Protein C Precursor Contains Signals for Intracellular Targeting

1992 • 35 citations

Human Surfactant Protein-C: Genetic Homogeneity and Expression in RDS; Comparison with Other Species

1994 • 27 citations

Familial desquamative interstitial pneumonitis occurring in infants

1987 • 22 citations

Alpha1-antitrypsin phenotypes in patients with cryptogenic fibrosing alveolitis: a case-control study

1997 • 18 citations

Diagnostic Advances in Idiopathic Pulmonary Fibrosis

1991 • 16 citations

Mapping of the Pulmonary Surfactant SP5 (SFTP2) Locus to 8p21 and Characterization of a Microsatellite Repeat Marker That Shows Frequent Loss of Heterozygosity in Human Carcinomas

1994 • 13 citations

Familial fibrocystic pulmonary dysplasia: a new case in a known affected family.

1966 • 7 citations

[A rare occurrence of familial idiopathic pulmonary fibrosis].

1993 • 1 citations