Assembly of Type IV Collagen

COLLAGENS: Molecular Biology, Diseases, and Potentials for Therapy

1995 • 1,599 citations

Structure and biological activity of basement membrane proteins

1989 • 967 citations

A Network Model for the Organization of Type IV Collagen Molecules in Basement Membranes

1981 • 889 citations

Type IV collagen: structure, gene organization, and role in human diseases. Molecular basis of Goodpasture and Alport syndromes and diffuse leiomyomatosis.

1993 • 610 citations

Basement Membrane Proteins: Structure, Assembly, and Cellular Interactions

1992 • 584 citations

Collagen IV alpha 3, alpha 4, and alpha 5 chains in rodent basal laminae: sequence, distribution, association with laminins, and developmental switches.

1994 • 403 citations

Collagen COL4A3 knockout: a mouse model for autosomal Alport syndrome.

1996 • 374 citations

Basement membrane structure in situ: evidence for lateral associations in the type IV collagen network.

1987 • 342 citations

Molecular and functional defects in kidneys of mice lacking collagen alpha 3(IV): implications for Alport syndrome.

1996 • 310 citations

Isoform switching of type IV collagen is developmentally arrested in X-linked Alport syndrome leading to increased susceptibility of renal basement membranes to endoproteolysis.

1997 • 307 citations

Differential expression of two basement membrane collagen genes, COL4A6 and COL4A5, demonstrated by immunofluorescence staining using peptide-specific monoclonal antibodies.

1995 • 277 citations

Glomerular Basement Membrane

1998 • 226 citations

Alport Syndrome: An Inherited Disorder of Renal, Ocular, and Cochlear Basement Membranes

1999 • 207 citations

Expression and function of heat shock protein 47: A collagen-specific molecular chaperone in the endoplasmic reticulum

1998 • 192 citations

Molecular genetics of Alport syndrome

1993 • 190 citations

Susceptibility to anti-glomerular basement membrane disease and Goodpasture syndrome is linked to MHC class II genes and the emergence of T cell-mediated immunity in mice.

1997 • 177 citations

Autosomal recessive Alport syndrome: Immunohistochemical study of type IV collagen chain distribution

1995 • 173 citations

Identification of the alpha 3 chain of type IV collagen as the common autoantigen in antibasement membrane disease and Goodpasture syndrome.

1995 • 168 citations

Alport syndrome

1996 • 156 citations

Alport syndrome and thin glomerular basement membrane disease.

1998 • 135 citations

The clinical spectrum of hereditary nephritis

1985 • 128 citations

Immunohistochemical study of α1-5 chains of type IV collagen in hereditary nephritis

1994 • 122 citations

Comparative distribution of the alpha 1(IV), alpha 5(IV), and alpha 6(IV) collagen chains in normal human adult and fetal tissues and in kidneys from X-linked Alport syndrome patients.

1995 • 116 citations

Goodpasture syndrome. Localization of the epitope for the autoantibodies to the carboxyl-terminal region of the alpha 3(IV) chain of basement membrane collagen.

1991 • 101 citations

Structural heterogeneity of the noncollagenous domain of basement membrane collagen.

1988 • 95 citations

The pathogenesis of Alport syndrome involves type IV collagen molecules containing the α3(IV) chain: Evidence from anti-GBM nephritis after renal transplantation

1992 • 92 citations

Specificity of Goodpasture autoantibodies for the recombinant noncollagenous domains of human type IV collagen.

1993 • 91 citations

The alpha 3 chain of type IV collagen induces autoimmune Goodpasture syndrome.

1994 • 90 citations

Seminiferous Tubule Basement Membrane

1997 • 89 citations

Glomerular basement membrane. Identification of dimeric subunits of the noncollagenous domain (hexamer) of collagen IV and the Goodpasture antigen

1991 • 80 citations

The Goodpasture Autoantigen

1996 • 78 citations

Evidence for separate networks of classical and novel basement membrane collagen. Characterization of alpha 3(IV)-alport antigen heterodimer.

1992 • 73 citations

The structural organization of type IV collagen. Identification of three NC1 populations in the glomerular basement membrane.

1992 • 64 citations

Immunohistochemical localization of basement membrane collagens and associated proteins in the murine cochlea

1996 • 62 citations

Substrate Recognition of Collagen-specific Molecular Chaperone HSP47

1999 • 60 citations

COL4A5 gene deletion and production of post-transplant anti-α3(IV) collagen alloantibodies in Alport syndrome

1994 • 58 citations

Structure and Biology of the Globular Domain of Basement Membrane Type IV Collagena

1985 • 56 citations

Expression of basement membrane type IV collagen chains during postnatal development in the murine cochlea

1996 • 51 citations

Bovine renal glomerular basement membrane. Assessment of proteolysis during isolation

1976 • 51 citations

Posttransplant anti-glomerular basement membrane nephritis in related males with Alport syndrome.

1990 • 49 citations

Alport Syndrome: From Bedside to Genome to Bedside

1993 • 48 citations

A COL4A3 gene mutation and post-transplant anti-α3(IV) collagen alloantibodies in Alport syndrome

1995 • 40 citations

A monoclonal antibody marker for Alport syndrome identifies the Alport antigen as the α5 chain of type IV collagen

1994 • 37 citations

Hsp47 and Other ER-Resident Molecular Chaperones Form Heterocomplexes with Each Other and with Collagen Type IV Chains

1996 • 32 citations

Type IV Collagen of Engelbreth-Holm-Swarm Tumor Matrix: Identification of Constituent Chains

1992 • 31 citations

Expression of type IV collagen alpha 3 and alpha 4 chain mRNA in X-linked Alport syndrome.

1996 • 28 citations

Different immunologic properties of the globular NC1 domain of collagen type IV isolated from various human basement membranes

1992 • 17 citations

Inherited diseases of the kidney

1993 • 5 citations