Deficiency of electron transfer flavoprotein or electron transfer flavoprotein:ubiquinone oxidoreductase in glutaric acidemia type II fibroblasts.

PROTEIN MEASUREMENT WITH THE FOLIN PHENOL REAGENT

1951 • 319,299 citations

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

1970 • 253,849 citations

Electrophoretic transfer of proteins from polyacrylamide gels to nitrocellulose sheets: procedure and some applications.

1979 • 54,907 citations

Short-Term Effects of Nose-Only Cigarette Smoke Exposure on Glutathione Redox Homeostasis, Cytochrome P450 1A1/2 and Respiratory Enzyme Activities in Mice Tissues

2013 • 47,043 citations

“Western Blotting”: Electrophoretic transfer of proteins from sodium dodecyl sulfate-polyacrylamide gels to unmodified nitrocellulose and radiographic detection with antibody and radioiodinated protein A

1981 • 8,657 citations

Glutaric aciduria type II: Report on a previously undescribed metabolic disorder

1976 • 229 citations

Glutaric aciduria Type II

1980 • 214 citations

A new iron-sulfur flavoprotein of the respiratory chain. A component of the fatty acid beta oxidation pathway

1977 • 210 citations

ON THE MECHANISM OF DEHYDROGENATION OF FATTY ACYL DERIVATIVES OF COENZYME A

1956 • 188 citations

Separation and properties of five distinct acyl-CoA dehydrogenases from rat liver mitochondria. Identification of a new 2-methyl branched chain acyl-CoA dehydrogenase.

1983 • 171 citations

[8] Kinetic analysis of progress curves

1979 • 170 citations

Multiple Acyl-CoA Dehydrogenase Deficiency (Glutaric Aciduria Type II) with Transient Hypersarcosinemia and Sarcosinuria; Possible Inherited Deficiency of an Electron Transfer Flavoprotein

1980 • 97 citations

General acyl-CoA dehydrogenase from pig liver. Kinetic and binding studies.

1979 • 81 citations

Immunological evidence for deficiency in an activator protein for sulfatide sulfatase in a variant form of metachromatic leukodystrophy.

1983 • 81 citations

Glutaric acidaemia type II (multiple Acyl‐Coa dehydrogenation deficiency)

1984 • 77 citations

Electron transfer flavoprotein from pig liver mitochondria. A simple purification and re-evaluation of some of the molecular properties

1983 • 68 citations

Solubilization and Electron Transfer Flavoprotein Requirement of Mitochondrial Sarcosine Dehydrogenase and Dimethylglycine Dehydrogenase

1961 • 67 citations

Biochemical studies in a patient with defects in the metabolism of acyl‐CoA and sarcosine: Another possible case of glutaric aciduria type II

1980 • 63 citations

Glutaric acidemia type II: Clinical, biochemical, and morphologic considerations

1982 • 63 citations

Subunit structure of electron transfer flavoprotein.

1983 • 58 citations

Glutaric acidemia type II: A form with deleterious intrauterine effects

1983 • 54 citations

The effects of pH, ionic strength, and chemical modifications on the reaction of electron transfer flavoprotein with an acyl coenzyme A dehydrogenase.

1983 • 44 citations

Glutaric Aciduria Type II. In Vitro Studies on Substrate Oxidation, Acyl-CoA Dehydrogenases, and Electron-Transferring Flavoprotein in Cultured Skin Fibroblasts

1980 • 38 citations

Neonatal glutaric aciduria type II: An X-linked recessive inherited disorder

1981 • 38 citations

Multiple acyl-Co A dehydrogenation deficiency (MADD) in a boy with nonketotic hypoglycemia, hepatomegaly, muscle hypotonia and cardiomyopathy. Detection of N-isovalerylglutamic acid and its monoamide.

1983 • 34 citations

Leucine catabolism during the differentiation of 3T3-L1 cells. Expression of a mitochondrial enzyme system.

1983 • 27 citations

The pattern of iron—sulfur centers in brown adipose tissue mitochondria: Preponderance of ETF dehydrogenase and invariance with the thermogenic state

1976 • 24 citations

Electron-transferring Flavoprotein Deficiency in the Multiple Acyl-CoA Dehydrogenation Disorders, Glutaric Aciduria Type II and Ethylmalonic—adipic Aciduria

1984 • 11 citations