Relationship between the two immunologically distinguishable forms of glucocerebrosidase in tissue extracts

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1988 • 7,933 citations

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1965 • 800 citations

Gaucher's Disease: Deficiency of “cid”β-Glucosidase and Reconstitution of Enzyme Activity In Vitro

1971 • 257 citations

A Deficiency of Glucocerebrosidase in Gaucher's Disease

1965 • 248 citations

Molecular cloning and nucleotide sequence of human glucocerebrosidase cDNA.

1985 • 209 citations

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1986 • 208 citations

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1985 • 139 citations

Enzyme replacement therapy in Gaucher's disease: large-scale purification of glucocerebrosidase suitable for human administration.

1977 • 133 citations

Human placental neuraminidase

1985 • 132 citations

Nucleotide sequence of cDNA containing the complete coding sequence for human lysosomal glucocerebrosidase.

1986 • 129 citations

Structure of the N-asparagine-linked oligosaccharide units of human placental beta-glucocerebrosidase.

1984 • 125 citations

Mutations of glucocerebrosidase: discrimination of neurologic and non-neurologic phenotypes of Gaucher disease.

1982 • 121 citations

Purification and properties of a heat-stable glucocerebrosidase activating factor from control and Gaucher spleen.

1977 • 118 citations

Isolation of cDNA clones for human β-glucocerebrosidase using the λgtll expression system

1984 • 72 citations

The occurrence of two immunologically distinguishable beta-glucocerebrosidases in human spleen

1985 • 71 citations

A procedure for the rapid purification in high yield of human glucocerebrosidase using immunoaffinity chromatography with monoclonal antibodies

1986 • 65 citations

Monoclonal Antibodies against Human β‐Glucocerebrosidase

1983 • 51 citations

Purification of β-glucocerebrosidase by preparative-scale high-performance liquid chromatography: The use of ethylene glycol-containing buffers for chromatography of hydrophobic glycoprotein enzymes

1985 • 46 citations

Human lysosomal β-glucosidase: Kinetic characterization of the catalytic, aglycon, and hydrophobic binding sites

1984 • 45 citations

Modification of subunit interaction in membrane‐bound acid β‐glucosidase from Gaucher disease

1983 • 41 citations

Isolation of heat-stable glucocerebrosidase activators from the spleens of three variants of Gaucher's disease

1977 • 40 citations

Deficient activity of glucocerebrosidase in urine from patients with type 1 Gaucher disease

1986 • 37 citations

Further studies on the activation of glucocerebrosidase by a heat-stable factor from Gaucher spleen

1985 • 35 citations

The cohydrolases in human spleen that stimulate glucosyl ceramide β-glucosidase

1983 • 34 citations

Characterization of the phospholipid requirement of a rat liver β-glucosidase

1984 • 32 citations

Propriétés des formes moléculaires de la β-glucosidase et de la β-glucocéréhrosidase de rate humaine normale et de maladie de Gaucher

2005 • 32 citations

Studies on a sphingolipid activator protein ( SAP-2) in fibroblasts from patients with lysosomal storage diseases, including Niemann-Pick disease Type C

1985 • 31 citations

Human lysosomal β-glucosidase: Purification by affinity chromatography

1984 • 30 citations

Purification of glucosylceramidase by affinity chromatography

1982 • 26 citations

Immunological Studies on Lysosomal Sphingomyelinase: Immunization Procedures, Properties of Polyclonal and Monoclonal Antibodies Obtained and Effect of Triton X-100 on Binding of Enzyme Activity

1986 • 4 citations