Application of magnetic chromatography to the isolation of lysosomes from fibroblasts of patients with lysosomal storage disorders

[2] Citrate synthase from rat liver

1969 • 435 citations

Analysis of high-resolution two-dimensional electrophoresis of differentiation-dependent alterations in cytosolic protein pattern of HL-60 leukemic cells

1990 • 139 citations

Delivery to lysosomes in the human carcinoma cell line HEp-2 involves an actin filament-facilitated fusion between mature endosomes and preexisting lysosomes.

1995 • 122 citations

Characterization of lysosomes isolated from Dictyostelium discoideum by magnetic fractionation.

1993 • 94 citations

Late onset GM2-gangliosidosis: Clinical, pathological, and biochemical studies on 8 patients

1973 • 94 citations

Second messengers regulate endosomal acidification in Swiss 3T3 fibroblasts.

1992 • 89 citations

Role of lysosomal acid ceramidase in the metabolism of ceramide in human skin fibroblasts

1981 • 54 citations

Biosynthesis, Processing, and Intracellular Transport of GM2 Activator Protein in Human Epidermal Keratinocytes

1997 • 43 citations

Prenatal diagnosis of Hurler disease by analysis of α‐iduronidase in chorionic villi

1991 • 29 citations

Defective lysosomal release of glycoprotein-derived sialic acid in fibroblasts from patients with sialic acid storage disease

1988 • 27 citations

Purification of lysosomal membrane proteins from human placenta.

1996 • 22 citations

Interaction of rat liver lysosomal membranes with actin.

1984 • 22 citations

N-Acetylneuraminic acid accumulation in a buoyant lysosomal fraction of cultured fibroblasts from patients with infantile generalized N-acetylneuraminic acid storage disease

1986 • 21 citations

Abnormal cathepsin B activity in Batten disease

1988 • 19 citations

A 5' splice site mutation in fucosidosis.

1993 • 18 citations

Secondary lysosomes as an integral part of the cytoskeleton: A morphological study in rat Kupffer cells

1990 • 17 citations

Ligand-specific isolation of endosomes and lysosomes using superparamagnetic colloidal iron dextran glycoconjugates and high gradient magnetic affinity chromatography.

1991 • 7 citations