New patterns of inheritance in mitochondrial disease

Sequence and organization of the human mitochondrial genome

1981 • 9,348 citations

THE UBIQUITIN SYSTEM

1998 • 8,360 citations

Mitochondrial DNA and human evolution

1987 • 2,967 citations

Mitochondrial genome variation and the origin of modern humans

2000 • 1,535 citations

Maternal inheritance of human mitochondrial DNA.

1980 • 1,327 citations

Uniparental inheritance of mitochondrial and chloroplast genes: mechanisms and evolution.

1995 • 896 citations

The Inheritance of Genes in Mitochondria and Chloroplasts: Laws, Mechanisms, and Models

2001 • 770 citations

Paternal Inheritance of Mitochondrial DNA

2002 • 675 citations

Paternal inheritance of mitochondrial DNA in mice

1991 • 674 citations

Ubiquitin tag for sperm mitochondria

1999 • 646 citations

Mitochondrial DNA content affects the fertilizability of human oocytes

2001 • 485 citations

Elimination of paternal mitochondrial DNA in intraspecific crosses during early mouse embryogenesis.

1995 • 466 citations

Ubiquitinated Sperm Mitochondria, Selective Proteolysis, and the Regulation of Mitochondrial Inheritance in Mammalian Embryos1

2000 • 425 citations

Exercise Intolerance Due to Mutations in the CytochromebGene of Mitochondrial DNA

1999 • 411 citations

Oxidative Stress and Mitochondrial DNA Mutations in Human Aging

1998 • 355 citations

The Molecular and Genetic Basis of Neurological Disease

1993 • 345 citations

Misconceptions about mitochondria and mammalian fertilization: Implications for theories on human evolution

1996 • 289 citations

Mammalian Mitochondria Possess Homologous DNA Recombination Activity

1996 • 275 citations

The Mutation Rate in the Human mtDNA Control Region

2000 • 246 citations

Maternal Inheritance of Mouse mtDNA in Interspecific Hybrids: Segregation of the Leaked Paternal mtDNA Followed by the Prevention of Subsequent Paternal Leakage

1998 • 233 citations

How clonal are human mitochondria?

1999 • 194 citations

A microdeletion in cytochrome c oxidase (COX) subunit III associated with COX deficiency and recurrent myoglobinuria

1996 • 193 citations

Mismatch repair activity in mammalian mitochondria

2003 • 179 citations

Paternal Leakage of Mitochondrial DNA in the Great Tit (Parus major)

2003 • 169 citations

Ubiquitination of Prohibitin in Mammalian Sperm Mitochondria: Possible Roles in the Regulation of Mitochondrial Inheritance and Sperm Quality Control1

2003 • 167 citations

Selective and Continuous Elimination of Mitochondria Microinjected Into Mouse Eggs From Spermatids, but Not From Liver Cells, Occurs Throughout Embryogenesis

2000 • 153 citations

Mitochondrial DNA in mammalian reproduction

1998 • 146 citations

Analysis of European mtDNAs for Recombination

2001 • 141 citations

A nonsense mutation (G15059A) in the cytochromeb gene in a patient with exercise intolerance and myoglobinuria

1999 • 115 citations

Mitochondrial DNA Content of Human Spermatozoa1

2003 • 106 citations

Recurrent myoglobinuria due to a nonsense mutation in the COX I gene of mitochondrial DNA

2000 • 105 citations

Early Degradation of Paternal Mitochondria in Domestic Pig (Sus scrofa) Is Prevented by Selective Proteasomal Inhibitors Lactacystin and MG1321

2003 • 103 citations

A novel gly290asp mitochondrial cytochromebmutation linked to a complex III deficiency in progressive exercise intolerance

1996 • 103 citations

mtDNA recombination in a natural population

1998 • 102 citations

No sex please, we're mitochondria: a hypothesis on the somatic unit of inheritance of mammalian mtDNA

2000 • 101 citations

Behaviour of a population of partially duplicated mitochondrial DNA molecules in cell culture: segregation, maintenance and recombination dependent upon nuclear background

1997 • 101 citations

The molecular and genetic basis of neurological disease

1993 • 95 citations

Does Human mtDNA Recombine?

2001 • 85 citations

Evaluation of Parental Mitochondrial Inheritance in Neonates Born after Intracytoplasmic Sperm Injection

1999 • 84 citations

IS ORGANELLE DNA STRICTLY MATERNALLY INHERITED? POWER ANALYSIS OF A BINOMIAL DISTRIBUTION

1992 • 72 citations

Recombination or mutation rate heterogeneity? Implications for Mitochondrial Eve

2003 • 66 citations

Mitochondrial Steve: paternal inheritance of mitochondria in humans

2003 • 56 citations

Do mitochondria recombine in humans?

2000 • 48 citations

Is Organelle DNA Strictly Maternally Inherited? Power Analysis of a Binomial Distribution

1992 • 24 citations

More review content in TREE 2003

2003 • 4 citations