Characterization of an Alternatively Spliced GM2 Activator Protein, GM2A Protein

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

1970 • 253,849 citations

Lysosomes in Biology and Pathology

1974 • 768 citations

The Use of Sep‐Pak™ C₁₈ Cartridges During the Isolation of Gangliosides

1980 • 472 citations

Saposins: structure, function, distribution, and molecular genetics.

1992 • 323 citations

AB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2.

1978 • 274 citations

Activator proteins and topology of lysosomal sphingolipid catabolism

1992 • 269 citations

Coding of Two Sphingolipid Activator Proteins (SAP-1 and SAP-2) by Same Genetic Locus

1988 • 251 citations

Purification and Characterization of an Activator Protein for the Degradation of Glycolipids G_M2and G_A2by Hexosaminidase A

1979 • 180 citations

Structure of Full-Length cDNA Coding for Sulfatide Activator, a Co-β-Glucosidase and Two Other Homologous Proteins: Two Alternate Forms of the Sulfatide Activator1

1989 • 134 citations

Hydrolysis of Tay-Sachs Ganglioside by β-Hexosaminidase A of Human Liver and Urine

1973 • 126 citations

The human GM2 activator protein. A substrate specific cofactor of beta-hexosaminidase A

1991 • 114 citations

The Precursor of Sulfatide Activator Protein is Processed to Three Different Proteins

1988 • 114 citations

Characterization of a nonspecific activator protein for the enzymatic hydrolysis of glycolipids.

1988 • 92 citations

A protein activator for the enzymic hydrolysis of GM2 ganglioside.

1981 • 83 citations

The Protein Activator Specific for the Enzymic Hydrolysis of GM₂ Ganglioside in Normal Human Brain and Brains of Three Types of GM₂ Gangliosidosis

1983 • 72 citations

Deficiency of the Hexosaminidase A Activator Protein in a Case of GM2 Gangliosidosis; Variant AB

1982 • 68 citations

Geometrical and Conformational Properties of Ganglioside GalNAc‐G_D1a, IV⁴GalNAcIV³Neu5AcII³Neu5AcGgOse₄Cer

1994 • 65 citations

[32] Labeled galactosyl ceramide and lactosyl ceramide

1972 • 61 citations

alpha-N-acetylgalactosaminidase from the limpet, Patella vulgata.

1977 • 61 citations

Isolation of a cDNA encoding the human G_M2 activator protein

1989 • 58 citations

Mapping of the gene coding for the human G_M2 activator protein to chromosome 5

1985 • 58 citations

The complete amino‐acid sequences of human ganglioside GM2 activator protein and cerebroside sulfate activator protein

1990 • 58 citations

Expression and specificity of human GM2 activator protein.

1994 • 54 citations

Characterization of full‐length cDNAs and the gene coding for the human GM2 activator protein

1991 • 54 citations

Molecular genetics of GM2-gangliosidosis AB variant: a novel mutation and expression in BHK cells

1993 • 51 citations

Degradation of gangliosides by the lysosomal sialidase requires an activator protein

1992 • 40 citations

Isolation and expression of a full-length cDNA encoding the human GM2 activator protein

1991 • 30 citations

Evidence for two cDNA clones encoding human GM2-activator protein

1992 • 21 citations

The Degradative Pathway of Gangliosides GM1 and GM2 in Neuro2a Cells by Sialidase

1995 • 20 citations

Specific Recognition of N-Acetylneuraminic Acid in the GM2 Epitope by Human GM2 Activator Protein

1995 • 18 citations