PEDIATRIC HEPATOLOGY

Universal Hepatitis B Vaccination in Taiwan and the Incidence of Hepatocellular Carcinoma in Children

1997 • 1,836 citations

Homozygous disruption of the murine MDR2 P-glycoprotein gene leads to a complete absence of phospholipid from bile and to liver disease

1993 • 1,437 citations

Alagille syndrome is caused by mutations in human Jagged1, which encodes a ligand for Notch1

1997 • 1,239 citations

HOMOTRANSPLANTATION OF THE LIVER IN HUMANS.

1963 • 1,170 citations

Mutations in the human Jagged1 gene are responsible for Alagille syndrome

1997 • 1,121 citations

Vertical Transmission of Hepatitis B Antigen in Taiwan

1975 • 1,022 citations

A gene encoding a liver-specific ABC transporter is mutated in progressive familial intrahepatic cholestasis

1998 • 980 citations

The Sister of P-glycoprotein Represents the Canalicular Bile Salt Export Pump of Mammalian Liver

1998 • 933 citations

A gene encoding a P-type ATPase mutated in two forms of hereditary cholestasis

1998 • 728 citations

Mutations in the MDR 3 gene cause progressive familial intrahepatic cholestasis

1998 • 718 citations

Molecular Pathogenesis of Cholestasis

1998 • 669 citations

Hepatic ductular hypoplasia associated with characteristic facies, vertebral malformations, retarded physical, mental, and sexual development, and cardiac murmur

1975 • 664 citations

Syndromic paucity of interlobular bile ducts (Alagille syndrome or arteriohepatic dysplasia): Review of 80 cases

1987 • 644 citations

Treatment of hereditary tyrosinaemia type I by inhibition of 4-hydroxyphenylpyruvate dioxygenase

1992 • 625 citations

Schiff's diseases of the liver

1999 • 441 citations

Identification of a new inborn error in bile acid synthesis: mutation of the oxysterol 7alpha-hydroxylase gene causes severe neonatal liver disease.

1998 • 350 citations

Genome screening by searching for shared segments: mapping a gene for benign recurrent intrahepatic cholestasis

1994 • 325 citations

Biliary atresia: Current concepts and research directions. Summary of a symposium

1996 • 318 citations

Pharmacological correction of neonatal lethal hepatic dysfunction in a murine model of hereditary tyrosinaemia type I

1995 • 304 citations

Seroepidemiology of hepatitis B virus infection in children: Ten years of mass vaccination in Taiwan

1996 • 296 citations

Efficacy of Hepatitis B Immune Globulin for Prevention of Perinatal Transmission of the Hepatitis B Virus Carrier State: Final Report of a Randomized Double-Blind, Placebo-Controlled Trial

1983 • 289 citations

AN INCREASED INCIDENCE OF EPSTEIN-BARR VIRUS INFECTION AND LYMPHOPROLIFERATIVE DISORDER IN YOUNG CHILDREN ON FK506 AFTER LIVER TRANSPLANTATION1

1995 • 275 citations

Byler disease. Fatal familial intrahepatic cholestasis in an Amish kindred.

1969 • 269 citations

Genetic and morphological findings in progressive familial intrahepatic cholestasis (Byler disease [PFIC-1] and Byler syndrome): Evidence for heterogeneity

1997 • 268 citations

Byler Disease

1969 • 250 citations

HEPATITIS B IMMUNE GLOBULIN (HBIG) EFFICACY IN THE INTERRUPTION OF PERINATAL TRANSMISSION OF HEPATITIS B VIRUS CARRIER STATE

1981 • 239 citations

Seroepidemiology of Hepatitis B Virus Infection in Children

1996 • 229 citations

Enzymic Differentiation in Mammalian Liver

1969 • 213 citations

Neonatal cholestasis

1985 • 208 citations

Liver Transplantation, Including the Concept of Reduced-size Liver Transplants in Children

1988 • 194 citations

Identification of a Locus for Progressive Familial Intrahepatic Cholestasis PFIC2on Chromosome 2q24

1997 • 188 citations

The role of mdr2 P‐glycoprotein in hepatobiliary lipid transport

1997 • 167 citations

Alagille syndrome.

1997 • 164 citations

Liver transplantation in pediatrics: Indications, contraindications, and pretransplant management

1991 • 146 citations

The significance of spontaneous hepatitis B e antigen seroconversion in childhood: With special emphasis on the clearance of hepatitis B e antigen before 3 years of age

1995 • 145 citations

Selective surgical management of progressive familial intrahepatic cholestasis (Byler's disease)

1995 • 140 citations

Long-term outcome after surgery for biliary atresia

1990 • 132 citations

Mapping of a locus for progressive familial intrahepatic cholestasis (Byler disease) to 18q21-q22, the benign recurrent intrahepatic cholestasis region

1995 • 132 citations

Immaturity of the enterohepatic circulation in early life: factors predisposing to "physiologic" maldigestion and cholestasis.

1983 • 119 citations

Seroepidemiologic Survey for Hepatitis B Virus Infection in Taiwan: The Effect of Hepatitis B Mass Immunization

1999 • 119 citations

FACTORS AFFECTING SURVIVAL AFTER ORTHOTOPIC LIVER TRANSPLANTATION IN INFANTS

1997 • 115 citations

Living related liver transplantation in children

1994 • 108 citations

Bile Acid Therapy in Pediatric Hepatobiliary Disease: The Role of Ursodeoxycholic Acid

1997 • 107 citations

Hepatitis B Virus Mutants with Precore-Region Defects in Two Babies with Fulminant Hepatitis and Their Mothers Positive for Antibody to Hepatitis B e Antigen

1991 • 105 citations

Nutrition During Infancy

1988 • 100 citations

Segmental orthotopic hepatic transplantation as a means to improve patient survival and diminish waiting-list mortality

1991 • 100 citations

Disorders of the Mitochondria

1998 • 99 citations

LIVER DISEASE IN INFANCY AND CHILDHOOD

1969 • 91 citations

Orthotopic Liver Transplantation for Congenital Biliary Atresia

1996 • 79 citations

Determinants of Bile Formation During Development: Ontogeny of Hepatic Bile Acid Metabolism and Transport

1987 • 75 citations

Immaturity of the Enterohepatic Circulation in Early Life

1983 • 68 citations

Focal glycogenosis of the liver in disorders of ureagenesis: Its occurrence and diagnostic significance

1997 • 68 citations

Improved survival in biliary atresia patients in the present era of liver transplantation

1993 • 68 citations

Alagille syndrome: family studies.

1995 • 62 citations

Bile acid transport across the hepatocyte cánalicular membrane

1997 • 60 citations

Electron microscopy and histochemistry of canalicular differentiation in fetal and neonatal rat liver

1972 • 56 citations

Lessons From the E-Ferol Tragedy

1986 • 54 citations

Inborn Errors of Metabolism in Children Referred With Reye's Syndrome

1988 • 51 citations

Hepatobiliary consequences of parenteral alimentation.

1990 • 50 citations

The significance of spontaneous hepatitis B e antigen seroconversion in childhood: With special emphasis on the clearance of hepatitis B e antigen before 3 years of age*1

1995 • 42 citations

Lessons from the E-Ferol tragedy.

1986 • 38 citations

INBORN ERRORS OF BILE ACID BIOSYNTHESIS AND TRANSPORT

1999 • 35 citations

Genetic disorders of mitochondrial fatty acid oxidation

1994 • 34 citations

Liver transplantation in children

1992 • 32 citations

The effect of immunosuppression on growth and development.

1995 • 30 citations

Liver transplantation from living donors

1994 • 29 citations

Treatment of extrahepatic bile duct atresia: results and long-term prognosis after hepatic portoenterostomy

1986 • 28 citations

Rapid Improvement in the Renal Tubular Dysfunction Associated With Tyrosinemia Following Hepatic Replacement

1992 • 25 citations

Tyrosinaemia type I: considerations of treatment strategy and experiences with risk assessment, diet and transplantation

1995 • 25 citations

Liver transplantation in children.

1992 • 23 citations

Rapid improvement in the renal tubular dysfunction associated with tyrosinemia following hepatic replacement.

1992 • 21 citations

Hepatobiliary, Pancreatic and Splenic Disease in Children: Medical and Surgical Management

1998 • 15 citations

Hepatobiliary, pancreatic and splenic disease in children : medical and surgical management

1997 • 13 citations

Development of organic anion transport in the liver

1996 • 9 citations

Living related liver transplantation in children

1995 • 7 citations

The canalicular bile salt exporting protein BSEP is not expressed in patients with progressive familial intrahepatic cholestasis type 2.

1998 • 7 citations

Treatment of extrahepatic bile duct atresia: Results and long-term prognosis after hepatic portoenterostomy

1986 • 4 citations

The SPGP gene, encoding the canalicular bile acid transporting protein SPGP/cBST, is not expressed in a subgroup of patients with progressive familial intrahepatic cholestasis (PFIC-2)

1998 • 3 citations