Carbohydrate Recognition Systems for Receptor-Mediated Pinocytosis

Functions of Lysosomes

1966 • 2,942 citations

Heritable Disorders of Connective Tissue

1960 • 1,560 citations

The synthesis of complex carbohydrates by multiglycosyltransferase systems and their potential function in intercellular adhesion

1970 • 1,208 citations

The Role of Surface Carbohydrates in the Hepatic Recognition and Transport of Circulating Glycoproteins

1974 • 1,200 citations

Transfer of proteins across membranes. II. Reconstitution of functional rough microsomes from heterologous components.

1975 • 1,175 citations

The Role of Sialic Acid in Determining the Survival of Glycoproteins in the Circulation

1971 • 1,061 citations

Transfer of Proteins Across Membranes

1981 • 894 citations

The Isolation and Properties of a Rabbit Liver Binding Protein Specific for Asialoglycoproteins

1974 • 614 citations

Evidence for receptor-mediated binding of glycoproteins, glycoconjugates, and lysosomal glycosidases by alveolar macrophages.

1978 • 593 citations

Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts.

1977 • 580 citations

Beta glucuronidase deficiency: Report of clinical, radiologic, and biochemical features of a new mucopolysaccharidosis

1973 • 498 citations

Physical and Chemical Studies on Ceruloplasmin

1968 • 468 citations

A hypothesis for I-cell disease: Defective hydrolases that do not enter lysosomes

1972 • 446 citations

Heritable disorders of connective tissue

1955 • 445 citations

The Binding of Desialylated Glycoproteins by Plasma Membranes of Rat Liver

1971 • 363 citations

Recognition and receptor-mediated uptake of a lysosomal enzyme, α-l-iduronidase, by cultured human fibroblasts

1977 • 354 citations

Isolation and characterization of a mannan-binding protein from rabbit serum

1980 • 329 citations

Inherited Disorders of Lysosomal Metabolism

1975 • 322 citations

A recognition marker required for uptake of a lysosomal enzyme by cultured fibroblasts

1974 • 281 citations

A beta-D-galactoside binding protein from electric organ tissue of Electrophorus electricus.

1975 • 277 citations

Subcellular membrane topology and turnover of a rat hepatic binding protein specific for asialoglycoproteins.

1979 • 259 citations

The Defect in the Hurler and Scheie Syndromes: Deficiency of α-L-Iduronidase

1972 • 244 citations

Chemical and physical properties of an hepatic membrane protein that specifically binds asialoglycoproteins.

1976 • 244 citations

The Defect in the Hunter Syndrome: Deficiency of Sulfoiduronate Sulfatase

1973 • 231 citations

Human β-glucuronidase: In vivo clearance and in vitro uptake by a glycoprotein recognition system on reticuloendothelial cells

1978 • 228 citations

Isolation and properties of beta-galactoside binding lectins of calf heart and lung.

1976 • 228 citations

Isolation and characterization of a mannan-binding protein from rabbit liver

1978 • 215 citations

The transport of lysosomal enzymes

1977 • 214 citations

Isolation and characterization of an avian hepatic binding protein specific for N-acetylglucosamine-terminated glycoproteins.

1977 • 206 citations

Plasma clearance of glycoproteins with terminal mannose and N-acetylglucosamine by liver non-parenchymal cells. Studies with β-glucuronidase, N-acetyl-β-<scp>d</scp>-glucosaminidase, ribonuclease B and agalacto-orosomucoid

1978 • 204 citations

Evidence for lysosomal enzyme recognition by human fibroblasts via a phosphorylated carbohydrate moiety

1978 • 185 citations

Physical and Chemical Studies on Ceruloplasmin

1970 • 183 citations

Phosphohexosyl recognition is a general characteristic of pinocytosis of lysosomal glycosidases by human fibroblasts.

1977 • 181 citations

Subcellular distribution of a mammalian hepatic binding protein specific for asialoglycoproteins.

1976 • 181 citations

Hepatic receptor that specifically binds oligosaccharides containing fucosyl α1→3 N -acetylglucosamine linkages

1978 • 171 citations

Mammalian Hepatic Lectin

1974 • 164 citations

Catabolism of Desialylated Ceruloplasmin in the Liver

1970 • 163 citations

Hepatic uptake of proteins coupled to fetuin glycopeptide

1971 • 157 citations

CORRECTIVE FACTORS FOR INBORN ERRORS OF MUCOPOLYSACCHARIDE METABOLISM

1971 • 156 citations

Effect of glycosylation on the in vivo circulating half-life of ribonuclease.

1976 • 151 citations

A hepatic receptor of avian origin capable of binding specifically modified glycoproteins.

1976 • 150 citations

Physical and Chemical Studies on Ceruloplasmin

1970 • 147 citations

Measurement of Circulating Desialylated Glycoproteins and Correlation with Hepatocellular Damage

1974 • 146 citations

Membrane glycoproteins and recognition phenomena

1977 • 141 citations

Direct demonstration of binding of a lysosomal enzyme, alpha-L-iduronidase, to receptors on cultured fibroblasts.

1979 • 140 citations

The Binding of Desialylated Glycoproteins by Plasma Membranes of Rat Liver

1972 • 138 citations

Absorption, Plasma Transport, and Cellular Retention of Cobalamin Analogues in the Rabbit

1977 • 136 citations

Hurler's syndrome, an a-L-iduronidase deficiency

1972 • 135 citations

A β-glucuronidase deficiency mucopolysaccharidosis: studies in cultured fibroblasts

1973 • 129 citations

The existence of a second route for the transfer of certain glycoproteins from the circulation into the liver

1976 • 112 citations

The Hurler Corrective Factor

1971 • 111 citations

Human plasma R-type vitamin B12-binding proteins. II. The role of transcobalamin I, transcobalamin III, and the normal granulocyte vitamin B12-binding protein in the plasma transport of vitamin B12.

1975 • 103 citations

Effect of reductive lactosamination on the hepatic uptake of bovine pancreatic ribonuclease A dimer.

1978 • 102 citations

The binding site of rabbit hepatic lectin.

1979 • 102 citations

Recognition of lysosomal glycosidases in vivo inhibited by modified glycoproteins

1976 • 102 citations

Invitro correction of deficient human fibroblasts by β-glucuronidase from different human sources

1974 • 101 citations

Inhibition of the rat clearance system for agalacto-orosomucoid by yeast mannans and by mannose

1977 • 100 citations

Evidence for specific recognition sites mediating clearance of lysosomal enzymes in vivo.

1976 • 100 citations

Specific adhesion of rat hepatocytes to beta-galactosides linked to polyacrylamide gels.

1978 • 99 citations

Isolation and properties of beta-D-galactoside-specific lectin from chick embryo thigh muscle.

1977 • 98 citations

Aglycosylantibody. Effects of exoglycosidase treatments on autochthonous antibody survival time in the circulation.

1976 • 98 citations

Carbohydrate structure of glycopeptides isolated from an hepatic membrane-binding protein specific for asialoglycoproteins.

1976 • 98 citations

Hunter's syndrome: A deficiency of L-idurono-sulfate sulfatase

1973 • 86 citations

Hepatic Binding Protein: The Protective Role of Its Sialic Acid Residues

1977 • 84 citations

Multiple isoelectric and recognition forms of human β-glucuronidase activity

1975 • 84 citations

Solitary cells and enzyme exchange in tetraparental mice

1976 • 82 citations

The binding of d-glucosyl-neoglycoproteins to the hepatic asialoglycoprotein receptor.

1978 • 79 citations

Excretion-Reuptake Route of β-Hexosaminidase in Normal and I-Cell Disease Cultured Fibroblasts

1979 • 76 citations

2-Deoxy-α-Ecdysone from Ovaries and Eggs of the Silkworm, Bombyx mori

1977 • 74 citations

Lymphocyte mitogenesis induced by a mammalian liver protein that specifically binds desialylated glycoproteins.

1977 • 70 citations

Reactivation of asialo-rabbit liver binding protein by resialylation with beta-D-galactoside alpha2 leads to 6 sialyltransferase

1977 • 70 citations

The role of glycosidically bound mannose in the assimilation of β-galactosidase by generalized gangliosidosis fibroblasts

1976 • 66 citations

Sphingolipidoses

1978 • 61 citations

Correlation of structural features of phosphomannans with their ability to inhibit pinocytosis of human beta-glucuronidase by human fibroblasts.

1978 • 57 citations

Human β-GIucuronidase. II. Fate of Infused Human Placental β-Glucuronidase in the Rat

1977 • 56 citations

Clearance of lysosomal hydrolases following intravenous infusion

1976 • 54 citations

Studies of the Metabolism of Asialotransferrins: Potentiation of the Catabolism of Human Asialotransferrin in the Rabbit

1974 • 53 citations

Studies on the Role of Glycosyltransferases in the Hepatic Binding of Asialoglycoproteins

1974 • 53 citations

Clearance of lysosomal hydrolases following intravenous infusion

1976 • 51 citations

The relationship of α-l-iduronidase and Hurler corrective factor

1976 • 49 citations

Receptor-mediated uptake of lysosomal enzymes.

1978 • 41 citations

Rat plasma clearance of horseradish peroxidase and yeast invertase is mediated by specific recognition

1978 • 39 citations

The Fate of the Plasma Membrane during Endocytosis

1977 • 33 citations

Differential uptake of human β-glucuronidase isoenzymes from spleen by deficient fibroblasts

1974 • 29 citations

Intercellular exchange of lysosomal enzymes: Enzyme assays in single human fibroblasts after co-cultivation

1976 • 27 citations

Human β-Glucuronidase. I. Recognition and Uptake by Animal Fibroblasts Suggests Animal Models for Enzyme Replacement Studies

1977 • 21 citations

The distribution of hydrolytic enzyme activities in human fibroblast cultures and their intercellular transfer

1978 • 19 citations

Identification of phosphoglycoproteins obtained from rat brain

1976 • 14 citations

31 P nuclear magnetic resonance studies on the phosphoglycopeptides obtained from rat brain glycoprotein

1976 • 10 citations

A functional role for lectins

1977 • 8 citations