Hypoglycemia in infancy and childhood. Part II

IMMUNOASSAY OF ENDOGENOUS PLASMA INSULIN IN MAN

1960 • 2,983 citations

The surgery of infancy and childhood

1953 • 1,413 citations

The Metabolic Basis of Inherited Disease.

1972 • 1,407 citations

SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY IN AN INFANT

1951 • 761 citations

Glucose-6-Phosphatase of the Liver in Glycogen Storage Disease

1952 • 574 citations

Growth and Growth Hormone

1968 • 435 citations

Carbohydrate Metabolism and Its Disorders.

1969 • 415 citations

Amino Acid Metabolism and Genetic Variation.

1968 • 263 citations

FAMILIAL HYPOGLYCEMIA PRECIPITATED BY AMINO ACIDS

1956 • 245 citations

Leigh's encephalomyelopathy: an inborn error of gluconeogenesis.

1968 • 201 citations

FASTING HYPOGLYCÆMIA AND METABOLIC ACIDOSIS ASSOCIATED WITH DEFICIENCY OF HEPATIC FRUCTOSE-1,6-DIPHOSPHATASE ACTIVITY

1970 • 200 citations

Beta cell nesidioblastosis in idiopathic hypoglycemia of infancy

1971 • 146 citations

An evaluation of seventy-five patients with hypopituitarism beginning in childhood

1965 • 144 citations

GLUCOSE-6-PHOSPHATASE DEFICIENCY GLYCOGEN STORAGE DISEASE

1962 • 143 citations

Spontaneous hypoglycemia

1955 • 140 citations

The Subgroups of Type III Glycogenosis

1967 • 135 citations

Plasma Insulin in Organic Hyperinsulinism: Comparative Effects of Tolbutamide, Leucine and Glucose1

1964 • 118 citations

Hepatic fructose-1,6-diphosphatase deficiency

1972 • 110 citations

Drug therapy in leucine-sensitive hypoglycemia

1964 • 107 citations

Relationships between glycogen storage disease and tophaceous gout

1967 • 98 citations

Ketotic hypoglycemia

1964 • 97 citations

Hypoglycemia

1937 • 95 citations

Surgical Diseases of the Pancreas

1988 • 94 citations

The Effect of a Benzothiadiazine, Diazoxide, on Carbohydrate Metabolism

1964 • 88 citations

Tumors associated with hypoglycemia—Pancreatic and extrapancreatic

1956 • 87 citations

Lactic acidosis with necrotizing encephalopathy in two sibs.

1965 • 82 citations

Leigh's subacute necrotizing encephalopathy: clinical and biochemical study, with special reference to therapy with lipoate.

1967 • 79 citations

Infantile Hypoglycaemia due to Inherited Deficiency of Glycogen Synthetase in Liver

1963 • 75 citations

Excessive production of uric acid in type I glycogen storage disease

1968 • 75 citations

STUDIES OF GLYCOGEN METABOLISM IN LIVER GLYCOGEN DISEASE (VON GIERKE'S DISEASE): SIX CASES WITH SIMILAR METABOLIC ABNORMALITIES AND RESPONSES TO GLUCAGON*

1961 • 72 citations

IDIOPATHIC SPONTANEOUS HYPOGLYCEMIA IN CHILDREN

1960 • 69 citations

The interrelationship of glycogen storage disease and gout

1965 • 66 citations

Deficient activity of dephosphophosphorylase kinase and accumulation of glycogen in the liver

1969 • 65 citations

THE EFFECT OF PORTACAVAL TRANSPOSITION ON CARBOHYDRATE METABOLISM: EXPERIMENTAL AND CLINICAL OBSERVATIONS.

1965 • 65 citations

STUDIES ON PATIENTS WITH ISLET-CELL TUMOR, INCLUDING THE PHENOMENON OF LEUCINE-INDUCED ACCENTUATION OF HYPOGLYCEMIA*

1961 • 62 citations

The Metabolic Basis of Inherited Disease

1961 • 62 citations

Type III Glycogenosis

1971 • 61 citations

CONTROL OF GLYCOGEN METABOLISM

1965 • 59 citations

Studies of uric acid metabolism in glycogen storage disease associated with gouty arthritis

1967 • 56 citations

PORTACAVAL TRANSPOSITION IN THE TREATMENT OF GLYCOGEN-STORAGE DISEASE

1966 • 56 citations

Diazoxide treatment of idiopathichypoglycemia of infancy

1967 • 53 citations

Glycogen Storage Disease

1961 • 51 citations

LEUCINE-INDUCED HYPOGLYCEMIA A REVIEW AND SPECULATIONS

1960 • 51 citations

Gluconeogenesis and insulin in the ketotic variety of childhood hypoglycemia and in control children

1969 • 51 citations

A possible role for the exocrine pancreas in the pathogenesis of neonatal leucine-sensitive hypoglycemia

1970 • 50 citations

SUBTOTAL PANCREATECTOMY IN THE MANAGEMENT OF SEVERE PERSISTENT IDIOPATHIC HYPOGLYCEMIA IN CHILDREN

1967 • 49 citations

Functional Differentiation of Glycogenoses of the Liver with Respect to the Use of Glycerol

1968 • 45 citations

FUNCTIONING ISLET CELL ADENOMA IN THE NEWBORN

1968 • 42 citations

Loss of cyclic 3′5′-AMP dependent kinase and reduction of phosphorylase kinase in skeletal muscle of a girl with deactivated phosphorylase and glycogenosis of liver and muscle

1970 • 41 citations

Serum Insulin Measurements in Children with Idiopathic Spontaneous Hypoglycemia and in Normal Infants, Children and Adults

1966 • 41 citations

Idiopathic hypoglycemia: A study of twenty-six children

1969 • 41 citations

Hypoglycemia and dwarfism associated with the isolated deficiency of growth hormone

1965 • 37 citations

Infantile lactic acidosis due to hereditary fructose 1,6-diphosphatase deficiency.

1971 • 37 citations

A Child with Lactacidemia and Fructose Diphosphatase Deficiency in the Liver

1971 • 37 citations

Cori's Disease (Amylo-1.6-Glucosidase Deficiency)

1963 • 36 citations

Islet cell adenomatosis and adenoma in an infant

1971 • 34 citations

Studies in the Relationship of Amino Acids to Infantile Hypoglycemia

1960 • 34 citations

SYMPTOMATIC HYPOGLYCEMIA, VISCERAL FATTY METAMORPHOSIS, AND AGLYCOGENOSIS IN AN INFANT LACKING GLYCOGEN SYNTHETASE AND PHOSPHORYLASE

1965 • 32 citations

Diazoxide in the Treatment of Infantile Hypoglycemia

1966 • 28 citations

EFFECT OF LEUCINE ON PLASMA INSULIN CONCENTRATION IN A GIRL WITH A PANCREATIC ADENOMA

1961 • 28 citations

Imbalance of liver phosphorylase and accumulation of hepatic glycogen in a girl with progressive disease of the brain

1965 • 28 citations

Liver glycogen disease

1964 • 26 citations

A Wernicke-like encephalomyelopathy in children (Leigh), an inborn error of metabolism? Report of 5 cases with emphasis on its familial incidence.

1965 • 25 citations

Zinc glucagon in the managementof idiopathic hypoglycemia

1963 • 25 citations

Diazoxide in the Management of Hypoglycemia in Infancy and Childhood

1969 • 24 citations

Congenital Islet Cell Adenoma Causing Hypoglycemia in a Newborn

1971 • 22 citations

Effects of Diazoxide Administration on Plasma Glucose, Insulin, and Lipids in Von Gierke's Disease

1966 • 20 citations

Hyperuricemia in childhood.

1968 • 20 citations

Studies of children with ketotic hypoglycemia.

1970 • 20 citations

Heterogeneous glycogen storage disease in siblings and favorable response to synthetic androgen administration

1962 • 19 citations

Glycogen-Storage Disease

1956 • 19 citations

Diazoxide in von Gierke's disease.

1968 • 18 citations

Tolbutamide Tolerance in Hypoglycemic Children

1964 • 18 citations

Hypopituitarism and Ketotic Hypoglycemia

1971 • 17 citations

Leucine-Sensitive Hypoglycemia Treated with Long-Acting Epinephrine

1965 • 16 citations

ENDOCRINOLOGY: Idiopathic hypoglycemia-a defect in hypothalamic ACTH-releasing factor secretion

1971 • 16 citations

Tolbutamide tolerance test and plasma-insulinresponse in children with idiopathic hypoglycemia

1967 • 15 citations

The glycogen storage diseases

1971 • 14 citations

Effects of infusion of ketones in children with ketotic hypoglycemia

1970 • 14 citations

Spontaneous Hyperinsulinism due to Benign Hyperplasia of Islet Cells

1959 • 13 citations

Surgical Therapy of Glycogen Storage Disease

1970 • 13 citations

LIVER DEGLYCOGENATION AFTER PORTACAVAL TRANSPOSITION.

1964 • 11 citations

The Use of Glucagon-Gel in Idiopathic Spontaneous Hypoglycemia of Infancy

1965 • 10 citations

Spontaneous Hypoglycemia Treated by Partial Pancreatectomy

1962 • 9 citations

CHRONIC HYPOGLYCEMIA IN AN INFANT TREATED BY SUBTOTAL PANCREATECTOMY

1952 • 9 citations

Pancreatic resection for hypoglycemia in children

1965 • 9 citations

Enzymatic Defects as Causes of Hypoglycemia

1965 • 8 citations

Symptomatic leucine sensitivity in a mother and daughter

1967 • 8 citations

In vitro studies of adipose tissue metabolism of glucose, glycerol and free fatty acids in glycogen storage disease type 1

1965 • 7 citations

ORGANIC HYPERINSULINISM

1953 • 6 citations

ACTION OF ALLOXAN ON A HYPOGLYCEMIC INFANT

1951 • 5 citations

Subtotal resection of the pancreas of an eight-year old child for hyperinsulinism.

1946 • 2 citations

Glycogen Storage Diseases

1968 • 1 citations

CLINICAL pathological conference; the Children's Medical Center, Boston, Massachusetts.

1958 • 1 citations