Hypertension and bilateral stenosis of the renal artery associated with congenital hypoplasia of the intrahepatic bile ducts

Hepatic ductular hypoplasia associated with characteristic facies, vertebral malformations, retarded physical, mental, and sexual development, and cardiac murmur

1975 • 664 citations

PRIMARY BILIARY CIRRHOSIS

1950 • 442 citations

Considerations of the pathogenesis of neonatal hepatitis, biliary atresia and choledochal cyst--the concept of infantile obstructive cholangiopathy.

1974 • 317 citations

Byler disease. Fatal familial intrahepatic cholestasis in an Amish kindred.

1969 • 269 citations

Arteriohepatic dysplasia: Familial pulmonary arterial stenosis with neonatal liver disease

1973 • 263 citations

Byler Disease

1969 • 250 citations

Pediatric Clinical Gastroenterology

1973 • 231 citations

Failure of bile acids to control hepatic cholesterogenesis: evidence for endogenous cholesterol feedback

1969 • 182 citations

Clinical Pathological Conference

1959 • 155 citations

Hypertriglyceridaemia Secondary to Liver Disease

1974 • 102 citations

XANTHOMATOUS BILIARY CIRRHOSIS (A CLINICAL SYNDROME)

1949 • 102 citations

Atresia of the intrahepatic dile ducts.

1951 • 83 citations

Cholestyramine therapy in patients with a paucity of intrahepatic bile ducts

1967 • 79 citations

Persistent jaundice in infancy

1962 • 71 citations

An electron microscopic and functional study of very low density lipoproteins in intestinal lymph

1970 • 71 citations

ATRESIA OF THE INTRAHEPATIC BILE DUCTS

1951 • 63 citations

FAMILIAL INTRAHEPATIC CHOLESTASIS WITH MENTAL AND GROWTH RETARDATION

1966 • 59 citations

Familial intrahepatic cholestatic jaundice in infancy.

1966 • 56 citations

Congenital Dysplasia of the Interlobular Bile Ducts With Extensive Skin Xanthomata: Congenital Acholangic Biliary Cirrhosis

1952 • 50 citations

Presence of An Intact Cholesterol Feedback Mechanism in the Liver in Biliary Stasis

1971 • 41 citations

STANDARDS FOR HEIGHT AND WEIGHT OF BRITISH CHILDREN FROM BIRTH TO MATURITY

1959 • 40 citations

Congenital Absence of the Intrahepatic Bile Ducts

1958 • 40 citations

Fatal Tuberculosis from BCG Vaccination

1955 • 38 citations

EFFECTS OF PHENOBARBITAL ON BILE SALT METABOLISM IN CHOLESTASIS DUE TO INTRAHEPATIC BILE DUCT HYPOPLASIA

1973 • 37 citations

Cholestyramine Therapy in Intrahepatic Biliary Atresia

1963 • 37 citations

Hypercholesterolemia and Hypertriglyceridemia in Children

1974 • 33 citations

CONGENITAL INTRAHEPATIC BILIARY ATRESIA

1956 • 30 citations

A Case of Familial Intrahepatic Cholestasis

1968 • 29 citations

Hypertriglyceridaemia Secondary to Liver Disease

1974 • 29 citations

CONGENITAL ATRESIA OF EXTRAHEPATIC BILE DUCTS

1954 • 27 citations

Congenital atresia of the extrahepatic bile ducts; report of 31 proved cases.

1953 • 25 citations

Congenital malformation of the bile ducts

1932 • 22 citations

Ein abnormes Low-density-Lipoprotein bei Cholestase

1970 • 22 citations

Congenital Biliary Hypoplasia

1964 • 21 citations

Hypercholesterolemia and hypertriglyceridemia in children

1974 • 21 citations

Absence of Interlobular Bile Ducts

1961 • 20 citations

Hypoplasia of Terminal Bile Ducts

1970 • 16 citations

Ein abnormes Low-density-Lipoprotein bei Cholestase. I. Isolierung und Charakterisierung

1970 • 13 citations

Pediatric Clinical Gastroenterology

1972 • 10 citations

INTRAHEPATIC BILIARY ATRESIA

1960 • 10 citations

Neonatal jaundice. A critical review of persistent obstructive jaundice in infancy.

1965 • 10 citations

Bile Duct Proliferation in Atresia and Related Hepatic Diseases

1967 • 9 citations

Familial recurrent intrahepatic cholestasis since early infancy

1971 • 7 citations

Zur Embryologie und angeborenen Hyperplasie der intrahepatischen Galleng�nge mit perilobul�rer und nodul�rer Leiberfibrose

1965 • 6 citations

Increased trihydroxycoprostanic acid in bile in familial intrahepatic biliary atresia

1973 • 6 citations

Atresia of the Intrahepatic Bile Ducts With Xanthomatosis

1967 • 6 citations

[Agenesis of the intrahepatic bile ducts].

1953 • 5 citations

[Congenital cysts of the common bile duct in the infant].

1953 • 5 citations

Increased trihydroxycoprostanic acid in bile in familial intrahepatic biliary atresia.

1973 • 5 citations

Cholestyramine therapy in patients with a paucity of intrahepatic bile ducts

1968 • 5 citations

Angeborener Verschluss der ausserhalb der Leber gelegenen Gallenwege

1928 • 4 citations

[Absence of intrahepatic bile ducts. A case].

1971 • 4 citations

[Familial jaundice caused by intrahepatic cholestasis].

1966 • 4 citations

[Agenesis of the intrahepatic biliary tract. Study of 9 personal cases].

1962 • 3 citations

[Hypoplasia of intrahepatic bile ducts with clinically benign course (author's transl)].

1973 • 3 citations

Intrahepatic biliary atresia with xanthomatosis

1966 • 3 citations

[Differential diagnosis "congenital bile duct atresia--neonatal hepatitis"].

1966 • 3 citations

[ON THE FAMILIAL PRESENCE OF INTRAHEPATIC BILE DUCT PROLIFERATIONS (CHOLANGIODYSPLASTIC PSEUDOCIRRHOSIS OF THE LIVER].

1964 • 2 citations

[Formation of terminal intrahepatic bile duct segments].

1951 • 2 citations

Hipoplasia de las vías biliares intrahepáticas

1959 • 2 citations

[Etiology, pathologic anatomy and pathogenesis of liver cirrhosis in infants].

1955 • 2 citations

[Hypoplasia of intrahepatic bile ducts and other forms of intrahepatic cholestasis in infancy (author's transl)].

1974 • 2 citations

Die Pathogenese der Hypercholesterol�mie nach Gallengangsverschlu�

1974 • 2 citations

The Children's Medical Center Boston, Mass.

1957 • 2 citations

Un cas de syndrome de MacMahon-Thannhauser congénital: modalité pathogénique particulière de l'agénésie biliaire intrahépatique.

1966 • 1 citations

[Congenital agenesis of intrahepatic bile ducts].

1962 • 1 citations

[Hypoplasia of the intrahepatic biliary tracts].

1965 • 1 citations

[AGENESIS OF THE INTRAHEPATIC BILE DUCTS. APROPOS OF A CASE].

1964 • 1 citations

[A case of agenesis of the intra-hepatic bile ducts].

1965 • 1 citations

Un cas d'agénésie des voies biliaires intra-hépatiques.

1965 • 1 citations

Intrahepatic biliary atresia associated wtih the presence of Australia-antigen.

1971 • 1 citations

[Serum lipoproteins and intrahepatic biliary tract atresia in children].

1971 • 1 citations

[A case of congenital MacMahon-Thannhauser syndrome: particular pathogenic mode of intrahepatic biliary agenesis].

1966 • 1 citations

[Diffuse-ray scintigraphy of the lung, a new radiologic method for evaluation of lung function in childhood].

1971 • 1 citations

[Atresia and agenesis of bile ducts].

1955 • 1 citations