Inherited Complement Deficiency States and SLE

The H-2 Major Histocompatibility Complex and the/Immune Response Region: Genetic Variation, Function, and Organization

1975 • 774 citations

Histocompatibility Testing, 1975

1976 • 736 citations

Systemic Lupus Erythematosus in the Community

1974 • 410 citations

HYDRALAZINE-INDUCED SYSTEMIC LUPUS ERYTHEMATOSUS: INFLUENCE OF HLA-DR AND SEX ON SUSCEPTIBILITY

1980 • 380 citations

Profiles of Antinuclear Antibodies in Systemic Rheumatic Diseases

1975 • 365 citations

Modulation of the classical pathway C3 convertase by plasma proteins C4 binding protein and C3b inactivator.

1979 • 338 citations

COMPLEMENT DEFICIENCY STATES

1978 • 334 citations

B-Lymphocyte Alloantigens Associated with Systemic Lupus Erythematosus

1978 • 293 citations

REACTIVE LYSIS: THE COMPLEMENT-MEDIATED LYSIS OF UNSENSITIZED CELLS

1970 • 275 citations

EVIDENCE FOR LINKAGE BETWEEN HL-A HISTOCOMPATIBILITY GENES AND THOSE INVOLVED IN THE SYNTHESIS OF THE SECOND COMPONENT OF COMPLEMENT

1974 • 261 citations

Neisseria meningitidis and Neisseria gonorrhoeae Bacteremia Associated with C6, C7, or C8 Deficiency

1979 • 259 citations

Lysis of RNA tumor viruses by human serum: direct antibody-independent triggering of the classical complement pathway.

1976 • 247 citations

Inherited deficiency of the second component of complement. Rheumatic disease associations.

1976 • 238 citations

Studies on human plasma C1 inactivator-enzyme interactions. I. Mechanisms of interaction with C1s, plasmin, and trypsin.

1975 • 219 citations

The Alternative Pathway of Complement Activation

1976 • 180 citations

Hereditary C2 Deficiency with Some Manifestations of Systemic Lupus Erythematosus

1972 • 170 citations

The Alternative Pathway of Complement — A System for Host Resistance to Microbial Infection

1980 • 169 citations

Anti-DNA activity in systemic lupus erythematosus. A diagnostic and therapeutic guide.

1971 • 157 citations

Hereditary deficiency of the fifth component of complement in man. I. Clinical, immunochemical, and family studies.

1976 • 137 citations

Epidemiologic studies on systemic lupus erythematosus comparative data for new york city and jefferson county, alabama, 1956–1965

1970 • 135 citations

C1r deficiency: an inborn error associated with cutaneous and renal disease

1972 • 127 citations

Immune Response of a Patient with Deficiency of the Fourth Component of Complement and Systemic Lupus Erythematosus

1979 • 119 citations

C2 Deficiency DEVELOPMENT OF LUPUS ERYTHEMATOSUS

1973 • 110 citations

The complement system in chronic glomerulonephritis: Three newly associated aberrations

1971 • 109 citations

Mixed lymphocyte culture determinants and C2 deficiency: LD-7a associated with C2 deficiency in four families.

1975 • 107 citations

Hereditary complement (C2) deficiency with dermatomyositis

1975 • 106 citations

Requirements for the solubilization of immune aggregates by complement. The role of the classical pathway.

1978 • 103 citations

Hereditary angioedema and “familial” lupus erythematosus in identical twin boys

1974 • 103 citations

Lupus-Erythematosus-like Syndrome with a Familial Defect of Complement

1972 • 98 citations

Linkage between the Gene (or Genes) Controlling Synthesis of the Fourth Component of Complement and the Major Histocompatibility Complex

1977 • 98 citations

DEFICIENCY OF C1r IN HUMAN SERUM

1970 • 90 citations

Severe systemic lupus erythematosus with nephritis in a boy with deficiency of the fourth component of complement

1977 • 87 citations

Hereditary deficiency of the third component of complement in a child with fever, skin rash, and arthralgias: Response to transfusion of whole blood

1977 • 86 citations

Deficiency of the second component of complement associated with anaphylactoid purpura and presence of mycoplasma in the serum.

1973 • 83 citations

Recurrent Septicemia Associated with Congenital Deficiency of C2 and Partial Deficiency of Factor B and the Alternative Complement Pathway

1978 • 82 citations

A Genetic Defect of the C1q Subcomponent of Complement Associated with Childhood (Immune Complex) Nephritis

1980 • 75 citations

Inherited C2 Deficiency and Systemic Lupus Erythematosus: Studies on a Family

1975 • 73 citations

Hereditary deficiency of the fifth component of complement in man. II. Biological properties of C5-deficient human serum.

1976 • 73 citations

Combined genetic deficiency of C6 and C7 in man.

1978 • 68 citations

Potassium Iodide Sensitivity in Four Patients with Hypocomplementemic Vasculitis

1979 • 66 citations

Selective deficiency of the second component of complement in a patient with anaphylactoid purpura

1975 • 66 citations

The chromosomal order of genes controlling the major histocompatibility complex, properdin factor B, and deficiency of the second component of complement.

1976 • 64 citations

Inherited deficiency of the ninth component of complement in man.

1980 • 61 citations

Biosynthetic Defect in Monocytes from Human Beings with Genetic Deficiency of the Second Component of Complement

1975 • 59 citations

Genetic Linkage Between the HL-A System and a Deficit of the Second Component (C2) of Complement

1975 • 57 citations

Absence of the Eighth Component of Complement in Association with Systemic Lupus Erythematosus-Like Disease

1977 • 53 citations

Deficiency of c7 with systemic lupus erythematosus. solubilization of immune complexes in complement‐deficient sera

1981 • 51 citations

Complement-human histocompatibility antigen haplotypes in C2 deficiency.

1981 • 51 citations

Activation of the alternative complement pathway by enveloped viruses containing limited amounts of sialic acid

1981 • 48 citations

Familial deficiency of two subunits of the first component of complement. c1r and c1s associated with a lupus erythematosus‐like disease

1978 • 46 citations

Deficiency of the Second Component of Complement (C2) with Chronic Vasculitis

1975 • 46 citations

A familial dysfunction of the eighth component of complement (C8)

1980 • 44 citations

Systemic lupus erythematosus, partial lipodystrophy and hypocomplementemia.

1979 • 44 citations

Hereditary C2 deficiency in systemic lupus erythematosus and acquired complement abnormalities in an unusual SLE-related syndrome.

1975 • 44 citations

Evidence for a Silent or Null Gene in Hereditary C2 Deficiency

1978 • 40 citations

Homozygous deficiency of the second component of complement presenting with recurrent bacterial meningitis.

1980 • 39 citations

Plasmapheresis in Hereditary Angioneurotic Edema and Systemic Lupus Erythematosus

1980 • 39 citations

Hereditary C2 deficiency. Association with skin lesions resembling the discoid lesion of systemic lupus erythematosus

1976 • 38 citations

Hereditary C4 deficiency--genetic studies and linkage to HLA.

1979 • 37 citations

Homozygous C2 deficiency with fulminant lupus erythematosus. severe nephritis via the alternative complement pathway

1978 • 36 citations

The autosomal recessive mode of inheritance of C1r deficiency in a large Puerto Rican family.

1974 • 35 citations

Humoral Immunity to Viruses

1979 • 34 citations

Hereditary C2 deficiency associated with cutaneous lupus erythematosus: clinical, laboratory, and genetic studies.

1979 • 34 citations

Hereditary C2 deficiency and systemic lupus erythematosus associated with severe glomerulonephritis.

1978 • 31 citations

Genetic deficiency of the second component of complement (C2) associated with systemic lupus erythematosus

1977 • 29 citations

Familial Late Complement Component (C6, C7) Deficiency With Chronic Meningococcemia

1980 • 28 citations

Lymphocytotoxic antibodies in systemic lupus erythematosus and clinically related diseases

1979 • 26 citations

Abstracts of Papers Presented at the Third International Complement Workshop, Harvard Medical School, Boston, Massachusetts, June 3–5, 1968

1968 • 24 citations

Inherited Deficiency of Second Component of Complement and HLA Haplotype A10,B18 Associated with Inflammatory Bowel Disease

1978 • 24 citations

Inborn Clr deficiency with a mild lupus-like syndrome

1979 • 23 citations

Recurrent meningococcal infections associated with a functional deficiency of the C8 component of human complement.

1980 • 23 citations

Hereditary C2 Deficiency Associated With Cutaneous Lupus Erythematosus

1979 • 22 citations

Deficiency of the second complement component association with the HLA haplotype A10, B18 in a normal population.

1982 • 21 citations

Hereditary Angioneurotic Oedema in Finland

1977 • 21 citations

Simultaneous occurrence of hereditary C6 and C2 deficiency in a French-Canadian family.

1979 • 21 citations

Studies on the C2-deficiency gene in man.

1980 • 20 citations

Lupus Erythematosus-like Syndrome With a Familial Deficiency of C2

1976 • 19 citations

Genetic Deficiencies of the Complement System

1972 • 18 citations

Hereditary C2 Deficiency Associated with Common Variable Immunodeficiency

1979 • 16 citations

The Croonian Lecture, 1980 - The complex proteases of the complement system

1980 • 15 citations

HLA ANTIGEN STUDIES IN A FAMILY WITH C2 DEFICIENCY

1976 • 15 citations

Identification of the α-γ subunit of the eighth component of complement (C8) in a patient with systemic lupus erythematosus and absent C8 activity: Patient and family studies

1982 • 14 citations

C3 metabolism in a patient with deficiency of the second component of complement (C2) and discoid lupus erythematosus.

1976 • 14 citations

Heterogeneity of the clinical syndrome in patients with systemic lupus erythematosus and genetic deficiency of the second complement component.

1978 • 13 citations

Familial discoid lupus erythematosus associated with heterozygote c2 deficiency

1980 • 12 citations

Deficiency of the second component of complement. Its occurrence with membranoproliferative glomerulonephritis.

1980 • 10 citations

Phagocytosis, Chemoluminescence, and Intracellular Killing of Fungi by Phagocytes from Subjects with Deficiency of the Second Component of Complement

1982 • 8 citations

Selective deficiencies in complement component : a family with hereditary C2 deficiency.

1978 • 8 citations

HLA-linked C2 deficiency in a Dutch patient with systemic lupus erythematosus.

1979 • 8 citations

Cases

1977 • 6 citations

Renal transplantation in a patient with hereditary deficiency of the second component of complement.

1981 • 4 citations

[Lupus erythematosus and hereditary lack of complement. Review of about one case of C2 deficit (author's transl)].

1977 • 3 citations

[Double C2 and C7 deficiency in the same subject: study of complement and HL-A system].

1978 • 2 citations

Deleted Work

1955 • 0 citations