Hereditary Elliptocytosis and Related Disorders

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

1970 • 253,849 citations

High resolution two-dimensional electrophoresis of proteins.

1975 • 19,515 citations

Electrophoretic analysis of the major polypeptides of the human erythrocyte membrane

1971 • 8,619 citations

The Metabolic Basis of Inherited Diseases

1972 • 1,762 citations

Selective solubilization of proteins and phospholipids from red blood cell membranes by nonionic detergents

1973 • 687 citations

Living Blood Cells and their Ultrastructure

1972 • 561 citations

Living Blood Cells and Their Ultrastructure

1974 • 556 citations

Ubiquitin is the ATP-dependent proteolysis factor I of rabbit reticulocytes.

1980 • 393 citations

Self‐Association of Human Spectrin

1978 • 339 citations

Theoretical and experimental studies on viscoelastic properties of erythrocyte membrane

1978 • 302 citations

Studies on the Destruction of Red Blood Cells

1943 • 298 citations

Interactions between membrane skeleton proteins and the intrinsic domain of the erythrocyte membrane

1982 • 235 citations

Intrinsic material properties of the erythrocyte membrane indicated by mechanical analysis of deformation

1975 • 224 citations

The influence of membrane skeleton on red cell deformability, membrane material properties, and shape.

1983 • 217 citations

Deficiency of skeletal membrane protein band 4.1 in homozygous hereditary elliptocytosis. Implications for erythrocyte membrane stability.

1981 • 210 citations

The molecular organization of the red cell membrane skeleton.

1983 • 206 citations

Absence of the major sialoglycoprotein in the membrane of human En(a--) erythrocytes and increased glycosylation of band 3.

1976 • 204 citations

Membrane skeletal dynamics: role in modulation of red cell deformability, mobility of transmembrane proteins, and shape.

1983 • 196 citations

Erythrocyte membranes 3. Recent clinical and experimental advances

1985 • 184 citations

Erythrocyte membrane tropomyosin. Purification and properties.

1984 • 180 citations

Deficient Red-Cell Spectrin in Severe, Recessively Inherited Spherocytosis

1982 • 179 citations

Red cell membrane skeletal defects in hereditary and acquired hemolytic anemias.

1983 • 169 citations

Factors predicting long-term survival in diffuse mixed, histiocytic, or undifferentiated lymphoma

1981 • 163 citations

Physiological shear stresses enhance the Ca2+ permeability of human erythrocytes

1981 • 162 citations

The Molecular Basis for Membrane – Cytoskeleton Association in Human Erythrocytes

1982 • 157 citations

Altered spectrin dimer-dimer association and instability of erythrocyte membrane skeletons in hereditary pyropoikilocytosis.

1981 • 148 citations

A protein immunologically related to erythrocyte band 4.1 is found on stress fibres of non-erythroid cells

1982 • 146 citations

STUDIES ON THE DESTRUCTION OF RED BLOOD CELLS. IV

1948 • 131 citations

Two individuals with elliptocytic red cells apparently lack three minor erythrocyte membrane sialoglycoproteins

1984 • 131 citations

Spectrin tetramer–dimer equilibrium and the stability of erythrocyte membrane skeletons

1980 • 130 citations

A solid-liquid composite model of the red cell membrane

1976 • 129 citations

A Genetic Defect in the Binding of Protein 4.1 to Spectrin in a Kindred with Hereditary Spherocytosis

1982 • 125 citations

A technique to detect reduced mechanical stability of red cell membranes: relevance to elliptocytic disorders

1982 • 124 citations

A Congenital Haemolytic Anaemia with Thermal Sensitivity of the Erythrocyte Membrane

1975 • 121 citations

Detection of a variant of protein 3, the major transmembrane protein of the human erythrocyte.

1977 • 121 citations

Structural characterization of the phosphorylation sites of human erythrocyte spectrin.

1980 • 118 citations

Synthesis and assembly of spectrin during avian erythropoiesis: Stoichiometric assembly but unequal synthesis of α and β spectrin

1983 • 112 citations

Defective spectrin dimer-dimer association with hereditary elliptocytosis.

1982 • 111 citations

Oligomeric states of spectrin in normal erythrocyte membranes: Biochemical and electron microscopic studies

1984 • 100 citations

Molecular and functional changes in spectrin from patients with hereditary pyropoikilocytosis.

1983 • 96 citations

Identification of the molecular defect in the erythrocyte membrane skeleton of some kindreds with hereditary spherocytosis

1982 • 94 citations

Erythrocyte membrane skeletal protein bands 4.1 a and b are sequence-related phosphoproteins.

1982 • 76 citations

Molecular Defect of Spectrin in Hereditary Pyropoikilocytosis

1982 • 73 citations

The effect of endogenous proteases on the spectrin binding proteins of human erythrocytes

1980 • 71 citations

Decreased membrane deformability in Melanesian ovalocytes from Papua New Guinea.

1984 • 70 citations

Sulfhydryl reagents induce altered spectrin self-association, skeletal instability, and increased thermal sensitivity of red cells

1983 • 70 citations

Red cell membrane in hemolytic disease Studies on variables affecting electrophoretic analysis

1979 • 67 citations

Elliptical Human Red Corpuscles

1904 • 66 citations

Glycoconnectin (PAS 2), a membrane attachment site for the human erythrocyte cytoskeleton.

1981 • 65 citations

Spectrin beta-chain variant associated with hereditary elliptocytosis.

1982 • 64 citations

Immunobiology of the Erythrocyte

1981 • 64 citations

A molecular defect in two families with hemolytic poikilocytic anemia: reduction of high affinity membrane binding sites for ankyrin.

1981 • 61 citations

A molecular defect of spectrin in a subset of patients with hereditary elliptocytosis. Alterations in the alpha-subunit domain involved in spectrin self-association.

1984 • 59 citations

Functional characterization of human erythrocyte spectrin .alpha. and .beta. chains: association with actin and erythrocyte protein 4.1

1984 • 58 citations

Erythrocyte membrane sidedness in lectin control of the Ca2+–A23187-mediated diskocyte ⇄ echinocyte conversion

1981 • 58 citations

Elliptocytosis with hemolytic anemia: the effects of splenectomy.

1955 • 57 citations

Effects of the calcium-mediated enzymatic cross-linking of membrane proteins on cellular deformability

1981 • 55 citations

Involvement of spectrin and ATP in infection of resealed erythrocyte ghosts by the human malarial parasite, Plasmodium falciparum.

1982 • 52 citations

Hemoglobin enhances the self-association of spectrin heterodimers in human erythrocytes.

1984 • 51 citations

Effect of heat on the circular dichroism of spectrin in hereditary pyropoikilocytosis.

1979 • 51 citations

ELLIPTIC ERYTHROCYTES IN MAN

1941 • 51 citations

Vesicle production on heated and stressed erythrocytes

1978 • 46 citations

The Life Span of the Elliptocyte

1954 • 46 citations

Altered assembly of spectrin in red cell membranes in hereditary pyropoikilocytosis

1981 • 45 citations

Spectrin tetramer-dimer equilibrium in hereditary elliptocytosis

1982 • 45 citations

Sarcomas routinely produced from putatively nontumorigenic Balb/3T3 and C3H/10T1/2 cells by subcutaneous inoculation attached to plastic platelets

1976 • 44 citations

Defective spectrin dimer–dimer association in a family with transfusion dependent homozygous hereditary elliptocytosis

1983 • 44 citations

Elliptical erythrocyte membrane skeletons and heat-sensitive spectrin in hereditary elliptocytosis.

1981 • 42 citations

The heterozygous form of 4.1(-) hereditary elliptocytosis [the 4.1(-) trait]

1985 • 42 citations

Membrane protein organization in ATP‐depleted and irreversibly sickled red cells

1979 • 41 citations

Molecular heterogeneity of hereditary pyropoikilocytosis: identification of a second variant of the spectrin alpha-subunit

1983 • 41 citations

Spectrin: structure, function, and abnormalities.

1983 • 40 citations

Analysis of the red cell membrane in a family with hereditary elliptocytosis — total or partial of protein 4.1

1981 • 39 citations

Heat‐Induced Erythrocyte Fragmentation in Neonatal Elliptocytosis

1979 • 39 citations

Tryptic digestion of spectrin in variants of hereditary elliptocytosis.

1981 • 38 citations

The band 3-rich membrane of llama erythrocytes: Studies on cell shape and the organization of membrane proteins

1983 • 38 citations

Common structural polymorphisms in human erythrocyte spectrin.

1984 • 36 citations

Defective binding of spectrin to ankyrin in a kindred with recessively inherited hereditary elliptocytosis.

1984 • 36 citations

HEREDITARY ELLIPTOCYTOSIS: AN UNUSUAL PRESENTATION OF HEMOLYSIS IN THE NEWBORN ASSOCIATED WITH TRANSIENT MORPHOLOGIC ABNORMALITIES

1969 • 35 citations

Inhibition of malarial invasion of red cells by chemical and immunochemical linking of spectrin molecules

1983 • 34 citations

Red cell calcium leak in congenital hemolytic anemia with extreme microcytosis

1976 • 33 citations

Hereditary elliptocytosis in two Maltese families

1961 • 32 citations

Autosomal dominant hemolytic anemia characterized by ovalocytosis

1965 • 30 citations

Hereditary Elliptocytosis with a Spectrin Molecular Defect in a White Patient

1984 • 28 citations

Hematologic Study of Three Generations of a White Family Showing Elliptical Erythrocytes

1929 • 25 citations

Shape and Shape Transformation of Heated Human Red Cells

1949 • 24 citations

Erythrocyte Membrane Elasticity, Fragmentation and Lysis

1978 • 23 citations

A shortened variant of red cell membrane protein 4.1

1982 • 23 citations

Hereditary elliptocytosis with hemolytic anemia

1963 • 22 citations

[1st instance of the absence of an erythrocyte membrane protein (band 4(1)) in a case of familial elliptocytic anemia].

1980 • 22 citations

Viscosity of human red cell membrane in plastic flow

1976 • 20 citations

Die Genese der Ovalocyten¹

1935 • 20 citations

Die Elliptocytose (Ovalocytose) und ihre klinische Bedeutung

1938 • 18 citations

Pyknocytosis in a Neonate: An Unusual Presentation of Hereditary Elliptocytosis

1977 • 18 citations

Hereditary Haemolytic Anaemia associated with Elliptocytosis: a Study of Three Families

1961 • 16 citations

Homozygous Hereditary Elliptocytosis as the Cause of Haemolytic Anemia in Infancy

1968 • 16 citations

HEREDITARY ELLIPTOCYTIC HAEMOLYTIC ANAEMIA

1958 • 15 citations

Hereditary Elliptocytosis in Iceland

1967 • 15 citations

Hereditary elliptocytosis and hyperhaemolysis. A comparative study of 6 families with 145 patients.

1966 • 13 citations

Hereditary Elliptocytosis and Hyperhaemolysis

1966 • 12 citations

Hereditary elliptical stomatocytosis: A case report

1976 • 8 citations

Hereditary Haemolytic Ovalocytosis with Defective Erythropoiesis

1979 • 7 citations

Red cell membrane skeleton: structure-function relationships.

1980 • 7 citations

The Genetic Basis of Hereditary Elliptocytosis With Hemolysis

1968 • 7 citations

Hereditary elliptocytosis with hemolytic anemia--a family study of five affected members.

1969 • 6 citations

Increased heat sensitivity of red blood cells in hereditary elliptocytosis with acquired cobalamin (vitamin B12) deficiency

1982 • 4 citations

Defective membrane skeleton assembly in hereditary elliptocytosis.

1981 • 4 citations

Hereditary Elliptocytosis in a Peruvian Family

1957 • 3 citations