Abnormal Respiratory Epithelial Ion Transport in Cystic Fibrosis

Chloride impermeability in cystic fibrosis

1983 • 750 citations

Pulmonary edema.

1974 • 642 citations

Increased Bioelectric Potential Difference across Respiratory Epithelia in Cystic Fibrosis

1981 • 578 citations

Localization of cystic fibrosis locus to human chromosome 7cen–q22

1985 • 498 citations

Abnormal Ion Permeation Through Cystic Fibrosis Respiratory Epithelium

1983 • 493 citations

A closely linked genetic marker for cystic fibrosis

1985 • 463 citations

Clinical aspects of mucociliary transport.

1977 • 367 citations

Effects of adrenaline and of spontaneous labour on the secretion and absorption of lung liquid in the fetal lamb.

1983 • 338 citations

A polymorphic DNA marker linked to cystic fibrosis is located on chromosome 7

1985 • 332 citations

The Role of Catecholamines in Lung Liquid Absorption at Birth

1978 • 325 citations

Ion fluxes across the pulmonary epithelium and the secretion of lung liquid in the foetal lamb

1974 • 323 citations

Defective beta adrenergic response of cystic fibrosis sweat glands in vivo and in vitro.

1984 • 296 citations

Relative ion permeability of normal and cystic fibrosis nasal epithelium.

1983 • 278 citations

Transepithelial transport by pulmonary alveolar type II cells in primary culture.

1982 • 269 citations

Commentary from Westminster

1981 • 251 citations

Immunologic and Neuropharmacologic Stimulation of Mucous Glycoprotein Release from Human Airways In Vitro

1980 • 235 citations

Higher Bioelectric Potentials Due to Decreased Chloride Absorption in the Sweat Glands of Patients with Cystic Fibrosis

1983 • 232 citations

Pancreatic Fluid Secretion and Protein Hyperconcentration in Cystic Fibrosis

1985 • 225 citations

A hypothesis for pulmonary clearance and its implications.

1968 • 211 citations

Cystic fibrosis decreases the apical membrane chloride permeability of monolayers cultured from cells of tracheal epithelium.

1985 • 201 citations

COMPOSITION OF TRACHEOBRONCHIAL SECRETIONS IN CYSTIC FIBROSIS OF THE PANCREAS AND BRONCHIECTASIS

1959 • 198 citations

Growth and differentiation of human nasal epithelial cells in culture. Serum-free, hormone-supplemented medium and proteoglycan synthesis.

1985 • 169 citations

Bioelectric properties and ion flow across excised human bronchi

1984 • 164 citations

Water and Electrolytes in Cervical Mucus from Patients with Cystic Fibrosis

1973 • 163 citations

Measurements of nasal transepithelial electric potential differences in normal human subjects in vivo.

1981 • 158 citations

Micropuncture studies of the sweat formation in cystic fibrosis patients

1969 • 140 citations

Active transport of Na+ and Cl- across the canine tracheal epithelium in vitro.

1975 • 133 citations

PULMONARY SUMPS, DUST ACCUMULATIONS, ALVEOLAR FLUID AND LYMPH VESSELS

1955 • 128 citations

Evidence for active Na+ transport by cultured monolayers of pulmonary alveolar epithelial cells

1983 • 126 citations

Culture of human nasal epithelial cells on collagen matrix supports. A comparison of bioelectric properties of normal and cystic fibrosis epithelia.

1985 • 109 citations

Composition and control of secretions from tracheal bronchial submucosal glands

1979 • 107 citations

Micropipette measurement of airway submucosal gland secretion. Autonomic effects.

1980 • 100 citations

Effect of tracheostomy on lung development in fetal lambs

1983 • 94 citations

Clearance of Inhaled Particles From the Human Nose

1973 • 94 citations

The variable effect of a bronchodilating agent on pulmonary function in cystic fibrosis

1973 • 84 citations

Fluid and Electrolyte Abnormalities in Exocrine Glands in Cystic Fibrosis

1983 • 83 citations

Studies on pulmonary secretions. II. Osmolality and the ionic environment of pulmonary secretions from patients with cystic fibrosis, bronchiectasis, and laryngectomy.

1967 • 77 citations

Bioelectric properties and ion transport of airways excised from adult and fetal sheep

1983 • 74 citations

Measurements of transepithelial electric potential differences in the trachea and bronchi of human subjects in vivo.

1982 • 70 citations

Biochemistry and rheology of sputum in asthma

1971 • 65 citations

Kartagener's Syndrome

1972 • 65 citations

A Review. Cystic Fibrosis at Forty—Quo Vadis?

1980 • 65 citations

PERSISTENCE OF ABNORMAL CHLORIDE ION PERMEABILITY IN CYSTIC FIBROSIS NASAL EPITHELIAL CELLS IN HETEROLOGOUS CULTURE

1985 • 65 citations

Increased nasal potential difference and amiloride sensitivity in neonates with cystic fibrosis

1986 • 58 citations

The Paradoxical Effect of Adrenergic and Methylxanthine Drugs in Cystic Fibrosis

1976 • 58 citations

Epithelial dysfunction in cystic fibrosis lung disease

1983 • 49 citations

Chloride uptake into cultured airway epithelial cells from cystic fibrosis patients and normal individuals.

1985 • 48 citations

The mucous lining of major bronchi in the rabbit lung.

1977 • 45 citations

Pulmonary airway clearance mechanisms: a reappraisal.

1977 • 39 citations

A comparative study of inhaled atropine sulfate and isoproterenol hydrochloride in cystic fibrosis.

1979 • 38 citations

THE ELECTROLYTE AND PROTEIN CONTENTS AND OUTPUTS IN DUODENAL JUICE AFTER PANCREOZYMIN AND SECRETIN STIMULATION IN NORMAL CHILDREN AND IN PATIENTS ITH CYSTIC FIBROSIS.1

1970 • 35 citations

Mineral composition of meconium

1966 • 34 citations

Effects of amphotericin B on ion and fluid movement across dog tracheal epithelium

1983 • 31 citations

Aldosterone Metabolism and Transepithelial Potential Difference in Normal and Cystic Fibrosis Subjects

1985 • 29 citations

Differing luminal potential difference of cystic fibrosis and control sweat secretory coils in vitro

1984 • 19 citations

Pathophysiology of Pulmonary Disease in Cystic Fibrosis

1985 • 14 citations

Boies Fundamentals of Otolaryngology

1990 • 9 citations

Human and Baboon Bronchial Sodium Absorption: Implications for Airway Fluid Movement and the Mucociliary Clearance Mechanism

1982 • 4 citations

SERUM IMMUNOREACTIVE ERYTHROPOIETIN (siEP) IN CHILDREN WITH CYANOTIC AND ACYANOTIC HEART DISEASE

1987 • 2 citations

Modulation of nasal epithelial ion permeability in normal and cystic fibrosis subjects in vivo

1983 • 2 citations

Deleted Work

1955 • 0 citations