Hexosaminidase-A and Hexosamini-dase-B: Studies in Tay-Sachs' and Sandhoff's Disease
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Abstract
References (9)
Tay-Sachs Disease: Generalized Absence of a Beta-D- N -Acetylhexosaminidase Component
1969 • 707 citations
N-Acetyl-β-glucosaminidases in human spleen
1968 • 523 citations
Deficient hexosaminidase activity in an exceptional case of Tay-Sachs disease with additional storage of kidney globoside in visceral organs
1968 • 329 citations
Variation of β‐N‐acetylhexosaminidase‐pattern in Tay‐Sachs disease
1969 • 258 citations
Lysosomal hydrolases: Conversion of acidic to basic forms by neuraminidase
1971 • 148 citations
Demonstration of an alteration of ganglioside metabolism in Tay-Sachs disease
1969 • 133 citations
N-ACETYLHEXOSAMINIDASE ACTIVITIES IN TAY-SACHS DISEASE
1969 • 73 citations
Antibody against purified human hexosaminidase B cross-reacting with human hexosaminidase A
1972 • 44 citations
Immunological identity of human liver hexosaminidases A and B
1972 • 14 citations
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