Differential Concanavalin A binding of cystic fibrosis and normal liver α-L-fucosidase

The Metabolic Basis of Inherited Disease

1979 • 2,083 citations

Practical enzymology of the sphingolipidoses

1977 • 183 citations

Lectins: Their Chemistry and Application to Immunology

1977 • 169 citations

Human liver alpha-L-fucosidase. Purification, characterization, and immunochemical studies.

1975 • 128 citations

Genetic studies on cystic fibrosis in Hawaii.

1968 • 110 citations

Cystic fibrosis: Leakage of lysosomal enzymes and of alkaline phosphatase into the extracellular space

1977 • 52 citations

Interaction between Concanavalin A and brain lysosomal acid hydrolases

1974 • 40 citations

Carbohydrate composition of purified human liver ?-L-Fucosidase

1977 • 27 citations

Abnormal distribution of α-L-fucosidase in cystic fibrosis: Increased activity in skin fibroblasts

1977 • 27 citations

Altered isoenzyme patterns of liver α‐L‐fucosidase in cystic fibrosis

1976 • 20 citations

DIFFERENCES IN MONOSACCHARIDE COMPOSITION OF MEMBRANE GLYCOPEPTIDES FROM CYSTIC FIBROSIS AND CONTROL SKIN FIBROBLASTS

1977 • 19 citations

Purification and characterization of altered cystic fibrosis liver α‐L‐fucosidase

1978 • 16 citations