Pantetheinase Activity and Cysteamine Content in Cystinotic and Normal Fibroblasts and Leukocytes

PROTEIN MEASUREMENT WITH THE FOLIN PHENOL REAGENT

1951 • 319,299 citations

Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo.

1976 • 331 citations

THE USE OF LACTOBACILLUS ARABINOSUS IN THE MICROBIOLOGICAL DETERMINATION OF PANTOTHENIC ACID

1944 • 201 citations

Increased Cystine in Leukocytes from Individuals Homozygous and Heterozygous for Cystinosis

1967 • 172 citations

Metabolism of Sulfur Compounds

1975 • 153 citations

Cystine: Compartmentalization within Lysosomes in Cystinotic Leukocytes

1969 • 102 citations

Cysteine Oxygenase

1969 • 101 citations

Characteristics of the cysteinesulfinate-forming enzyme system in rat liver

1966 • 80 citations

Disulfide reduction in rat liver

1970 • 73 citations

ENZYMATIC DEGRADATION AND RESYNTHESIS OF COENZYME A

1954 • 69 citations

Metabolism of Coenzyme A

1975 • 66 citations

Cystinosis and the Fanconi Syndrome

1976 • 58 citations

Cystine metabolism in human fibroblasts. Comparison of normal, cystinotic, and gamma-glutamylcysteine synethetase-deficient cells.

1976 • 55 citations

Assay and Distribution of Bound Forms of Pantothenic Acid

1959 • 52 citations

The Enzymatic Oxidation of Cysteamine to Hypotaurine in the Presence of Sulfide

1963 • 48 citations

Distribution of glutathione reductase and detection of glutathione-cystine transhydrogenase in rat tissues

1968 • 40 citations

The degradative metabolism of <scp>l</scp>-cysteine and <scp>l</scp>-cystine in vitro by liver in cystinosis

1962 • 39 citations

THE METABOLISM OF AMINO ACIDS, PEPTIDES, AND DISULFIDES IN LYSOSOMES OF FIBROBLASTS CULTURED FROM NORMAL INDIVIDUALS AND THOSE WITH CYSTINOSIS

1970 • 38 citations

Ineffectiveness of Ascorbic Acid Therapy in Nephropathic Cystinosis

1979 • 35 citations

Distribution of glutathione-cystine transhydrogenase activity in subcellular fractions of rat intestinal mucosa

1969 • 32 citations

Disulfide reduction in rat liver. II. Chromatographic separation of nucleotide-dependent disulfide reductase and GSH-disulfide transhydrogenase activities of the high-speed supernatant fraction

1970 • 29 citations

DEFICIENCIES OF -SH-DEPENDENT ENZYMES IN CYSTINOSIS.

1965 • 28 citations

Enzymic Reduction of Cystine by Subcellular Fractions of Cultured and Peripheral Leukoyctes from Normal and Cystinotic Individuals

1972 • 25 citations

METABOLISM OF PANTETHINE IN THE RAT

1974 • 25 citations

Cystine, cysteine, and glutathione metabolism in normal and cystinotic fibroblasts in vitro, and in cultured normal amniotic fluid cells

1971 • 25 citations

Activity of some animal tissues on the oxidation of cysteamine to hypotaurine in the presence of sulphide.

1964 • 18 citations

A new pathway of taurine biosynthesis.

1976 • 18 citations

Determination of sulfite in biological fluids: The usefulness of radioactive N-ethylmaleimide

1968 • 11 citations

Investigations on Pantothenic Acid and its Related Compounds. II. Biochemical Studies. (1). Biosynthesis of Coenzyme A from Pantothenate, Pantethine and from S-Benzoylpantetheine in vitro and in vivo

1965 • 11 citations

A new method for the determination of enzymatic pantethine--splitting activity.

1970 • 8 citations

A pH-stat method for pantetheinase activity determination.

1976 • 7 citations

Enzymic reduction of cystine and glutathione in cultivated human fibroblast from normal subjects and patients with cystinosis.

1975 • 6 citations

Patterns of Cystine Reduction by Fibroblasts from Normal and Cystinotic Children

1977 • 6 citations

Pediococcus acidilactici NCIB 6990, a New Test Organism for Microbiological Assaying of Pantothenic Acid

1975 • 5 citations

In vitro enzymatic conversion of pantothenylcysteine-4'-phosphate into cysteamine.

1975 • 3 citations

The stereospecificity of enzymatic pantetheine hydrolysis.

1974 • 1 citations