Treatment of Carbamyl Phosphate Synthetase Deficiency with Keto Analogues of Essential Amino Acids

Modified Reagents for Determination of Urea and Ammonia

1962 • 3,743 citations

Adaptive Characteristics of Urea Cycle Enzymes in the Rat

1962 • 738 citations

Determination of Creatinine by Means of Automatic Chemical Analysis

1961 • 567 citations

Comparative Biochemistry of Urea Synthesis

1959 • 409 citations

The measurement of ammonia in whole blood, erythrocytes, and plasma.

1957 • 243 citations

A study of plasma free amino acid levels. II. Normal values for children and adults

1973 • 184 citations

The Effect of Keto-analogues of Essential Amino Acids in Severe Chronic Uremia

1973 • 183 citations

Synthesis of Essential Amino Acids from Their α-Keto Analogues by Perfused Rat Liver and Muscle

1973 • 128 citations

Metabolic and Genetic Studies of a Family with Ornithine Transcarbamylase Deficiency

1974 • 86 citations

Nitrogen Sparing Induced by a Mixture of Essential Amino Acids Given Chiefly as Their Keto-Analogues during Prolonged Starvation in Obese Subjects

1974 • 78 citations

Hyperammonaemia. A variant type of deficiency of liver ornithine transcarbamylase.

1969 • 65 citations

Lethal Neonatal Deficiency of Carbamyl Phosphate Synthetase

1974 • 59 citations

Congenital Hyperammonemia

1970 • 59 citations

Carbamylphosphate synthetase deficiency in an infant with severe cerebral damage.

1969 • 49 citations

Rapid Determination of Ammonia in a Perchloric Acid Supernate from Blood, by Use of an Ammonia-Specific Electrode

1973 • 47 citations

Inhibition of gluconeogenesis by α-oxo acids

1964 • 44 citations

Substitution of Five Essential Amino Acids by their Alpha-keto Analogues in the Diet of Rats

1974 • 42 citations

A Case of Carbamyl Phosphate Synthetase Deficiency

1972 • 35 citations

Plasma Glutamine and Oxypurine Content in Patients with Gout

1955 • 32 citations

Improved method for the estimation of plasma ammonia by ion exchange

1968 • 31 citations

Pathogenesis of maple-syrup-urine disease: observations during dietary management and treatment of coma by peritoneal dialysis

1969 • 28 citations

LETHAL NEONATAL HYPERAMMONÆMIA DUE TO COMPLETE ORNITHINE-TRANSCARBAMYLASE DEFICIENCY

1971 • 23 citations

X-LINKED TRANSMISSION OF ORNITHINE-TRANSCARBAMYLASE DEFICIENCY

1972 • 20 citations

Ornithine Transcarbamylase Deficiency

1975 • 12 citations

Estimation of micro amounts of carbamyl phosphate

1973 • 8 citations