Multiple defects of the respiratory chain including complex II in a family with myopathy and encephalopathy

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

1970 • 253,849 citations

A simplification of the protein assay method of Lowry et al. which is more generally applicable

1977 • 8,485 citations

Mitochondrial protein import

1989 • 820 citations

Familial mitochondrial encephalomyopathy (MERRF): Genetic, pathophysiological, and biochemical characterization of a mitochondrial DNA disease

1988 • 509 citations

[2] Citrate synthase from rat liver

1969 • 435 citations

Batch purification of ovomucoid and characterization of the purified product

1971 • 272 citations

[47] Mammalian succinate dehydrogenase

1978 • 256 citations

Succinate dehydrogenase. I. Purification, molecular properties, and substructure

1971 • 252 citations

A mitochondrial encephalomyopathy: the first case with an established defect at the level of coenzyme Q

1986 • 163 citations

Reconstitution of Succinate-Coenzyme Q Reductase (Complex II) and Succinate Oxidase Activities by a Highly Purified, Reactivated Succinate Dehydrogenase

1969 • 153 citations

Isolation of cytochrome b560 from complex II (succinateùbiquinone oxidoreductase) and its reconstitution with succinate dehydrogenase.

1980 • 119 citations

Fatal Lactic Acidosis in Infancy with a Defect of Complex III of the Respiratory Chain

1989 • 105 citations

Effect of iron deficiency on succinate- and NADH-ubiquinone oxidoreductases in skeletal muscle mitochondria.

1984 • 90 citations

Mitochondria1 encephalomyopathy with decreased succinate‐cytochrome c reductase activity

1984 • 87 citations

Peptides from complex II active in reconstitution of succinate-ubiquinone reductase.

1980 • 84 citations

Quantitation of rabbit cytochrome P-450, form 2, in microsomal preparations bound directly to nitrocellulose paper using a modified peroxidase-immunostaining procedure

1984 • 84 citations

Kearns-Sayre syndrome and complex II deficiency

1989 • 77 citations

[7] Preparation and properties of dihydroubiquinone: Cytochrome c oxidoreductase (complex III)

1978 • 74 citations

Mitochondrial membrane components. 8. Polypeptides in the succinate-coenzyme Q reductase segment of the respiratory chain

1977 • 63 citations

Effects of dietary iron deficiency on iron-sulfur proteins and bioenergetic functions of skeletal muscle mitochondria

1982 • 63 citations

The prosthetic groups of succinate dehydrogenase: 30 years from discovery to identification

1985 • 61 citations

Interrelations of reconstitution activity, reactions with electron acceptors, and iron-sulfur centers in succinate dehydrogenase

1977 • 58 citations

Advances in Contemporary Neurology

1989 • 58 citations

A mitochondrial myopathy with a defective respiratory chain and carnitine deficiency

1983 • 50 citations

Skeletal muscle mitochondrial β-oxidation. A study of the products of oxidation of [U-14C]hexadecanoate by h.p.l.c. using continuous on-line radiochemical detection

1988 • 44 citations

Mitochondrial myopathy with lactic acidosis and deficient activity of muscle succinate cytochrome-c-oxidoreductase

1984 • 38 citations

The site of synthesis of the iron-sulfur subunits of the flavoprotein and iron-protein fractions of human NADH dehydrogenase.

1988 • 31 citations

Biosynthesis and processing of the large and small subunits of succinate dehydrogenase in cultured mammalian cells

1987 • 8 citations