Defective oxidative metabolism of myodystrophic skeletal muscle mitochondria

PROTEIN MEASUREMENT WITH THE FOLIN PHENOL REAGENT

1951 • 319,299 citations

RESPIRATORY ENZYMES IN OXIDATIVE PHOSPHORYLATION

1955 • 1,457 citations

[15] Isolation of liver or kidney mitochondria

1967 • 1,096 citations

A CASE OF SEVERE HYPERMETABOLISM OF NONTHYROID ORIGIN WITH A DEFECT IN THE MAINTENANCE OF MITOCHONDRIAL RESPIRATORY CONTROL: A CORRELATED CLINICAL, BIOCHEMICAL, AND MORPHOLOGICAL STUDY

1962 • 943 citations

The Energy-linked Reaction of Calcium with Mitochondria

1965 • 556 citations

Determination of Organic Phosphorus Compounds by Phosphate Analysis

1956 • 510 citations

Carnitine Deficiency of Human Skeletal Muscle with Associated Lipid Storage Myopathy: A New Syndrome

1973 • 506 citations

Muscle Carnitine Palmityltransferase Deficiency and Myoglobinuria

1973 • 476 citations

Spectra and Reaction Kinetics of Respiratory Pigments of Homogenized and Intact Cells

1952 • 439 citations

RESPIRATORY ENZYMES IN OXIDATIVE PHOSPHORYLATION

1955 • 434 citations

Dystrophia Muscularis: A HEREDITARY PRIMARY MYOPATHY IN THE HOUSE MOUSE

1955 • 335 citations

On cytochrome c oxidase I. The extinction coefficients of cytochrome a and cytochrome a3

1966 • 326 citations

Biochemical and Osmotic Properties of Skeletal Muscle Mitochondria

1954 • 289 citations

Biochemical studies of skeletal muscle mitochondria

1968 • 193 citations

A Disorder of Muscle Lipid Metabolism and Myoglobinuria

1975 • 161 citations

[11] The preparation of heart mitochondria from laboratory animals

1967 • 150 citations

Trichopoliodystrophy

1972 • 140 citations

Luft's disease

1976 • 136 citations

A Cytochrome-Related Inherited Disorder of the Nervous System and Muscle

1970 • 118 citations

SKELETAL MUSCLE DISEASE WITH ABNORMAL MITOCHONDRIA

1967 • 117 citations

A Skeletal-Muscle Disorder Associated with Intermittent Symptoms and a Possible Defect of Lipid Metabolism

1970 • 115 citations

A generalized disorder of nervous system, skeletal muscle and heart resembling Refsum's disease and Hurler's syndrome

1967 • 108 citations

A generalized disorder of nervous system, skeletal muscle and heart resembling Refsum's disease and Hurler's syndrome

1967 • 86 citations

Neuromuscular Disorder Associated With a Defect in Mitochondrial Energy Supply

1976 • 84 citations

[68] Isolation and determination of ubiquinone

1967 • 81 citations

Progressive Ophthalmoplegia, Glycogen Storage, and Abnormal Mitochondria

1973 • 79 citations

Severe Hypermetabolism with Primary Abnormality of Skeletal Muscle Mitochondria

1971 • 74 citations

Myodystrophy, a New Myopathy on Chromosome 8 of the Mouse

1976 • 70 citations

On the mechanism of a calcium-associated defect of oxidative phosphorylation in progressive muscular dystrophy

1973 • 64 citations

Myopathy with abnormal structure and function of muscle mitochondria.

1967 • 61 citations

Mitochondria-Lipid-Glycogen (MLG) Disease of Muscle

1973 • 61 citations

Carnitine-palmityl-transferase deficiency

1976 • 56 citations

Oxidative phosphorylation and glycolysis in the hereditary muscular dystrophy of the Syrian hamster.

1967 • 33 citations

Differing Populations of Mitochondria Isolated from the Skeletal Muscle of Normal and Dystrophic Hamsters

1974 • 32 citations

Palmitic acid-1-¹⁴C oxidation by skeletal muscle mitochondria of dystrophic mice

1970 • 27 citations

Effect of ruthenium red on oxidative phosphorylation and the calcium and magnesium content of skeletal muscle mitochondria of normal and BIO 14.6 dystrophic hamsters

1973 • 26 citations

Fatty acid oxidation by skeletal muscle mithochondria in duchenne dystrophy

1972 • 25 citations

A magnesium-responsive defect of respiration and oxidative phosphorylation in skeletal muscle mitochondria of dystrophic hamsters

1970 • 25 citations

Myopathy with mitochondrial inclusion bodies: histological and metabolic studies

1974 • 20 citations

Acetyl-1-¹⁴C-l-carnitine Oxidation, Carnitine Acetyltransferase Activity, and CoA Content in Skeletal Muscle Mitochondria from Normal and Dystrophic Mice (Strain 129)

1972 • 13 citations

Luft's disease: An electron cytochemical study

1977 • 11 citations

Scanning electron microscopy and cytochemical localization of carnitine acetyltransferase activity in normal and dystrophic muscle of mice

1973 • 8 citations