Peroxisomal organization in normal and cerebrohepatorenal (Zellweger) syndrome fibroblasts.

Tissue fractionation studies. 6. Intracellular distribution patterns of enzymes in rat-liver tissue

1955 • 4,109 citations

Peroxisomes (microbodies and related particles).

1966 • 1,635 citations

A MICROSPECTROPHOTOMETRIC METHOD FOR THE DETERMINATION OF CYTOCHROME OXIDASE

1951 • 1,369 citations

A fatty acyl-CoA oxidizing system in rat liver peroxisomes; enhancement by clofibrate, a hypolipidemic drug.

1976 • 1,136 citations

THE LARGE-SCALE SEPARATION OF PEROXISOMES, MITOCHONDRIA, AND LYSOSOMES FROM THE LIVERS OF RATS INJECTED WITH TRITON WR-1339

1968 • 1,112 citations

ANALYTICAL STUDY OF MICROSOMES AND ISOLATED SUBCELLULAR MEMBRANES FROM RAT LIVER

1974 • 840 citations

Peroxisomal and Mitochondrial Defects in the Cerebro-Hepato-Renal Syndrome

1973 • 777 citations

Metabolic Pathways in Peroxisomes and Glyoxysomes

1981 • 558 citations

Adrenoleukodystrophy

1975 • 459 citations

Tissue fractionation studies. 15. Intracellular distribution and properties of β-N-acetylglucos-aminidase and β-galactosidase in rat liver

1960 • 379 citations

Characterization of a New Human Diploid Cell Strain, IMR-90

1977 • 371 citations

Two species of lysosomal organelles in cultured human fibroblasts

1979 • 360 citations

GLYCEROLIPID BIOSYNTHESIS IN PEROXISOMES VIA THE ACYL DIHYDROXYACETONE PHOSPHATE PATHWAY*

1982 • 347 citations

Tissue fractionation studies. 18. Resolution of mitochondrial fractions from rat liver into three distinct populations of cytoplasmic particles by means of density equilibration in various gradients

1964 • 346 citations

Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome)

1983 • 340 citations

The Cerebrohepatorenal (Zellweger) Syndrome

1984 • 268 citations

Cerebro-hepato-renal syndrome of Zellweger

1975 • 246 citations

Activity of peroxisomal enzymes and intracellular distribution of catalase in Zellweger syndrome

1984 • 200 citations

Deficiency of acyl-CoA: Dihydroxyacetone phosphate acyltransferase in patients with Zellweger (cerebro-hepato-renal) syndrome

1984 • 192 citations

The cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects

1983 • 183 citations

Cerebro-hepato-renal (Zellweger) syndrome and neonatal adrenoleukodystrophy: similarities in phenotype and accumulation of very long chain fatty acids.

1982 • 179 citations

Defects of Bile Acid Synthesis in Zellweger's Syndrome

1979 • 171 citations

Structure, composition, physical properties, and turnover of proliferated peroxisomes. A study of the trophic effects of Su-13437 on rat liver.

1975 • 162 citations

Microbodies: peroxisomes and glyoxysomes.

1981 • 159 citations

LYSOSOMES IN LYMPHOID TISSUE

1967 • 146 citations

ANALYTICAL FRACTIONATION OF HOMOGENATES FROM CULTURED RAT EMBRYO FIBROBLASTS

1974 • 135 citations

Adrenoleukodystrophy: Impaired oxidation of long chain fatty acids in cultured skin fibroblasts and adrenal cortex

1981 • 130 citations

Biosynthesis and intracellular transport of enzymes of peroxisomal beta-oxidation.

1984 • 124 citations

Peroxisomes (microbodies) in cell pathology.

1984 • 97 citations

Cytochemistry of human catalase. The demonstration of hepatic and renal peroxisomes by a high temperature procedure.

1979 • 94 citations

Acyl-Coa oxidase and hydratase-dehydrogenase, two enzymes of the peroxisomal beta-oxidation system, are synthesized on free polysomes of clofibrate-treated rat liver.

1984 • 88 citations

Cyanide-insensitive and clofibrate enhanced β -oxidation of dodecanedioic acid in rat liver an indication of peroxisomal β-oxidation of N-dicarboxylic acids

1982 • 77 citations

Implication of a peroxisomal enzyme in the catabolism of glutaryl-CoA

1984 • 74 citations

Biochemical Studies in the Liver and Muscle of Patients with Zellweger Syndrome

1983 • 73 citations

Very long chain fatty acid oxidation in rat liver

1981 • 61 citations

Acyl-CoA synthetase and the peroxisomal enzymes of β-oxidation in human liver. Quantitative analysis of their subcellular localization

1984 • 59 citations

MICROPEROXISOMES AND PEROXISOMES IN RELATION TO LIPID METABOLISM*

1982 • 58 citations

Isolation of lysosomal α-mannosidase mutants of Chinese hamster ovary cells

1979 • 57 citations

Palmityl-CoA oxidase: Detection in several guinea pig tissues and peroxisomal localisation in mucosa of small intestine

1980 • 54 citations

Licht- und Elektronenmikroskopische Leberbefunde beim Cerebro-Hepato-Renalen Syndrom nach Zellweger (Peroxisomen-Defizienz)

1979 • 45 citations

The resolution of two populations of lysosomal organelles containing endocytosed wistaria floribunda agglutinin from murine fibroblasts

1981 • 38 citations

Testicular feminization of the mouse: paucity of peroxisomes in Leydig cell of the testis.

1981 • 11 citations

LARGE‐SCALE CLINICAL TRIALS: ARE THEY WORTH THE COST?

1982 • 5 citations