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Screening and outcomes in biliary atresia: Summary of a National Institutes of Health workshop

Data up to Jan 2025

Published2007
Citations250
References127

Total Citations Per Year

Abstract

References (127)

Executive Summary

2006 • 472 citations

Reversal of Left-Right Asymmetry: a Situs Inversus Mutation

1993 • 470 citations

The frequency and outcome of biliary atresia in the UK and Ireland

2000 • 414 citations

A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000

2006 • 376 citations

Guideline for the Evaluation of Cholestatic Jaundice in Infants: Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition

2004 • 357 citations

Surgical treatment of biliary atresia

1968 • 342 citations

Five- and 10-year survival rates after surgery for biliary atresia: a report from the Japanese biliary atresia registry

2003 • 326 citations

Pathogenesis and Outcome of Biliary Atresia: Current Concepts

2003 • 293 citations

A new operation for 'non-correctable' biliary atresia : hepatic portoenterostomy

1959 • 292 citations

Seamless management of biliary atresia in England and Wales (1999–2002)

2004 • 281 citations

Prognosis of biliary atresia in the era of liver transplantation: French national study from 1986 to 1996

1999 • 273 citations

Identification and Functional Analysis of ZIC3 Mutations in Heterotaxy and Related Congenital Heart Defects

2004 • 261 citations

Biliary atresia splenic malformation syndrome: an etiologic and prognostic subgroup.

1993 • 255 citations

Serving the Family From Birth to the Medical Home

2000 • 244 citations

Detection of Group C Rotavirus in Infants with Extrahepatic Biliary Atresia

1996 • 242 citations

The biliary atresia splenic malformation syndrome: A 28-year single-center retrospective study

2006 • 239 citations

Risk Factors for Severe Hyperbilirubinemia in Neonates

2004 • 231 citations

Detection of reovirus RNA in hepatobiliary tissues from patients with extrahepatic biliary atresia and choledochal cysts

1998 • 229 citations

Biliary Atresia and Reovirus Type 3 Infection

1982 • 228 citations

Biliary atresia registry, 1976 to 1989

1990 • 222 citations

Group A Rotaviruses Produce Extrahepatic Biliary Obstruction in Orally Inoculated Newborn Mice

1993 • 221 citations

A Multivariable Risk Factor Analysis of the Portoenterostomy (Kasai) Procedure for Biliary Atresia

1997 • 212 citations

Biliary atresia: The King's College Hospital Experience (1974–1995)

1997 • 212 citations

Genetic induction of proinflammatory immunity in children with biliary atresia

2002 • 203 citations

Epidemiology of biliary atresia in France: a national study 1986–96

1999 • 201 citations

Biliary Atresia: Clinical Profiles, Risk Factors, and Outcomes of 755 Patients Listed for Liver Transplantation

2005 • 194 citations

Biliary Atresia Is Associated with CD4+ Th1 Cell–Mediated Portal Tract Inflammation

2004 • 191 citations

Anthropometric evaluation of children with chronic liver disease

1990 • 189 citations

Obstruction of extrahepatic bile ducts by lymphocytes is regulated by IFN-γ in experimental biliary atresia

2004 • 186 citations

Physiologic cholestasis: Elevation of the primary serum bile acid concentrations in normal infants

1981 • 182 citations

Obstruction of extrahepatic bile ducts by lymphocytes is regulated by IFN-γ in experimental biliary atresia

2004 • 173 citations

The Viral Association of Neonatal Cholestasis in Sweden: A Possible Link Between Cytomegalovirus Infection and Extrahepatic Biliary Atresia

1998 • 171 citations

Management of patients with biliary atresia in France: Results of a decentralized policy 1986-2002

2006 • 169 citations

Technique and results of operative management of biliary atresia

1978 • 156 citations

Long‐Term Prognosis of Patients with Biliary Atresia: A 25 Year Summary

2006 • 155 citations

Screening for Biliary Atresia by Infant Stool Color Card in Taiwan

2006 • 152 citations

Gilbert’s syndrome is a contributory factor in prolonged unconjugated hyperbilirubinemia of the newborn

1999 • 148 citations

The nature of malnutrition in children with end-stage liver disease awaiting orthotopic liver transplantation

1992 • 140 citations

Unraveling the Pathogenesis and Etiology of Biliary Atresia

2005 • 139 citations

New aspects in a murine model for extrahepatic biliary atresia

1997 • 136 citations

Nutritional support in children with end-stage liver disease: a randomized crossover trial of a branched-chain amino acid supplement

1992 • 136 citations

Extrahepatic biliary atresia: A disease or a phenotype?

2002 • 133 citations

Anomalous development of the hepatobiliary system in theinv mouse

1999 • 132 citations

A population-based study on the incidence and possible pre- and perinatal etiologic risk factors of biliary atresia

2002 • 125 citations

The significance of human jagged 1 mutations detected in severe cases of extrahepatic biliary atresia

2002 • 116 citations

U.S. Newborn Screening Policy Dilemmas for the Twenty-First Century

2001 • 115 citations

Extrahepatic biliary atresia and associated anomalies: Etiologic heterogeneity suggested by distinctive patterns of associations

1993 • 114 citations

COMPARATIVE STUDIES OF BILIARY ATRESIA IN THE HUMAN NEWBORN AND REOVIRUS‐INDUCED CHOLANGITIS IN WEANLING MICE

1982 • 113 citations

Congenital biliary atresia and jaundice in lambs and calves

1990 • 109 citations

Screening of newborn infants for cholestatic hepatobiliary disease with tandem mass spectrometry Commentary: What is tandem mass spectrometry?

1999 • 106 citations

Lack of Evidence for Rotavirus by Polymerase Chain Reaction/Enzyme Immunoassay of Hepatobiliary Samples from Children with Biliary Atresia

1997 • 98 citations

Long-term Survival Following Kasai Portoenterostomy: Is Chronic Liver Disease Inevitable?

2003 • 98 citations

Studies in the etiology of extrahepatic biliary atresia: Time-space clustering

1982 • 98 citations

Keratin 8 and 18 mutations are risk factors for developing liver disease of multiple etiologies

2003 • 96 citations

Making the diagnosis of biliary atresia using the triangular cord sign and gallbladder length

2000 • 95 citations

Biliary atresia: Should all patients undergo a portoenterostomy?

1997 • 95 citations

Identification, genomic organization, chromosomal mapping and mutation analysis of the human INV gene, the ortholog of a murine gene implicated in left-right axis development and biliary atresia

2001 • 92 citations

Congenital Structural Abnormalities in Biliary Atresia: Evidence for Etiopathogenic Heterogeneity and Therapeutic Implications

1991 • 92 citations

Biliary Atresia and Cytomegalovirus Infection: A DNA Study

1999 • 88 citations

Functional Outcomes of Pediatric Liver Transplantation

2003 • 88 citations

Body Composition and Components of Energy Expenditure in Children With End- Stage Liver Disease

2003 • 83 citations

Detection of Reovirus Type 3 in the Porta Hepatis of an Infant with Extrahepatic Biliary Atresia: Ultrastructural and Immunocytochemical Study

1984 • 83 citations

Coordinate expression of regulatory genes differentiates embryonic and perinatal forms of biliary atresia

2004 • 82 citations

Reovirus 3 not detected by reverse transcriptase—mediated polymerase chain reaction analysis of preserved tissue from infants with cholestatic liver disease

1995 • 79 citations

Serving the family from birth to the medical home. Newborn screening: a blueprint for the future - a call for a national agenda on state newborn screening programs

2000 • 77 citations

Outcome after Portoenterostomy in Biliary Atresia: Pivotal Role of Degree of Liver Fibrosis and Intensity of Stellate Cell Activation

2005 • 76 citations

Biliary atresia, cytomegalovirus, and age at referral.

1996 • 76 citations

Biliary Atresia Revisited

2004 • 73 citations

On Congenital Obliteration of the Bile-Ducts.

1892 • 72 citations

Biliary Atresia, Cytomegalovirus, and Age at Referral

1996 • 71 citations

Health-related quality of life in long-term survivors of pediatric liver transplantation

2000 • 69 citations

Pathogenesis and Treatment Opportunities for Biliary Atresia

2006 • 68 citations

Improved survival in biliary atresia patients in the present era of liver transplantation

1993 • 68 citations

The epidemiology of extrahepatic biliary atresia in New York State, 1983–98

2004 • 66 citations

Transcriptional profiling after bile duct ligation identifies PAI-1 as a contributor to cholestatic injury in mice

2005 • 63 citations

Enterohepatic circulation of nonconjugated bilirubin in rats fed with human milk

1991 • 62 citations

Population Screening for Neonatal Liver Disease: Potential for a Community-Based Programme

2003 • 62 citations

The Portoenterostomy Procedure for Biliary Atresia

1978 • 58 citations

Risk of Sepsis in Newborns With Severe Hyperbilirubinemia

1992 • 56 citations

The Role of Reovirus Type 3 Infection in an Established Murine Model for Biliary Atresia

2002 • 55 citations

Altered expression of genes involved in hepatic morphogenesis and fibrogenesis are identified by cDNA microarray analysis in biliary atresia

2003 • 54 citations

Pathogenesis and Outcome of Biliary Atresia: Current Concepts

2003 • 53 citations

Guideline for the Evaluation of Cholestatic Jaundice in Infants: Recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition

2004 • 53 citations

A Controlled, Randomized, Double-Blind Trial of Prophylaxis Against Jaundice Among Breastfed Newborns

2005 • 53 citations

Postoperative corticosteroid therapy for bile drainage in biliary atresia—a nationwide survey

2004 • 53 citations

Extrahepatic bile duct atresia and viral involvement

2005 • 52 citations

Japanese Biliary Atresia Registry, 1989 to 1994.

1997 • 51 citations

Association of the reovirus S1 gene with serotype 3-induced biliary atresia in mice

1994 • 50 citations

The intussusception antireflux valve is ineffective for preventing cholangitis in biliary atresia: a prospective study

2003 • 47 citations

Pathologic versus physiologic cholestasis: Elevated serum concentration of a secondary bile acid in the presence of hepatobiliary disease

1981 • 46 citations

Analysis of the Biliary Transcriptome in Experimental Biliary Atresia

2005 • 45 citations

Advances in treatment of biliary atresia

1983 • 44 citations

Reovirus serotype 3 infection in infants with extrahepatic biliary atresia or neonatal hepatitis

1994 • 43 citations

Analysis of the Biliary Transcriptome in Experimental Biliary Atresia

2005 • 42 citations

Molecular Control of Liver Development

2006 • 41 citations

Population Screening for Neonatal Liver Disease: A Feasibility Study

1998 • 40 citations

Treatment of biliary atresia: A study of our operative results

1981 • 37 citations

Body Composition of Children Aged 1 to 12 years with Biliary Atresia or Alagille Syndrome

2005 • 36 citations

Direct enzymatic assay of urinary sulfated bile acids to replace serum bilirubin testing for selective screening of neonatal cholestasis

1996 • 33 citations

Serum bile acid patterns in neonatal hepatitis and extrahepatic biliary atresia

1977 • 32 citations

Value of gamma-glutamyl transpeptidase for early diagnosis of biliary atresia.

1998 • 32 citations

A Valved Hepatic Portoduodenal Intestinal Conduit for Biliary Atresia

1991 • 29 citations

Effectiveness of an intussusceptive antireflux valve to prevent ascending cholangitis after hepatic portojejunostomy in biliary atresia

1991 • 29 citations

Does “Cystic” Biliary Atresia Represent a Distinct Clinical and Etiological Subgroup? A Series of Three Cases

2005 • 28 citations

Results of Surgery in 88 Consecutive Cases of Extrahepatic Biliary Atresia

1982 • 25 citations

Sulfated and Nonsulfated Bile Acids in Urine of Patients with Biliary Atresia

1986 • 22 citations

Body Composition and Components of Energy Expenditure in Children With End‐ Stage Liver Disease

2003 • 22 citations

Urinary bile acid profile in children with inborn errors of bile acid metabolism and chronic cholestasis; screening technique using electrospray tandem mass-spectrometry (ES/MS/MS).

2003 • 21 citations

Long‐term Survival Following Kasai Portoenterostomy: Is Chronic Liver Disease Inevitable?

2003 • 21 citations

The Kasai operation (hepatic portoenterostomy) for biliary atresia—Experience with 20 cases

1979 • 20 citations

Hepatic Protoenterostomy

1975 • 20 citations

Kasai portoenterostomy: Differences related to race

2001 • 18 citations

Urinary sulfated bile acid concentrations in infants with biliary atresia and breast‐feeding jaundice

2003 • 17 citations

Long-term results in treatment of biliary atresia.

1977 • 16 citations

Transcriptional reprogramming in murine liver defines the physiologic consequences of biliary obstruction

2003 • 16 citations

Biliary atresia: which factors predict the success of a Kasai operation? An analysis of 36 patients.

2000 • 16 citations

The Viral Association of Neonatal Cholestasis in Sweden: A Possible Link Between Cytomegalovirus Infection and Extrahepatic Biliary Atresia

1998 • 14 citations

Pre‐ and postoperative nutritional care in liver transplantation in children

1996 • 13 citations

Pre‐ and postoperative nutritional care in liver transplantation in children

1996 • 13 citations

Serum bile acid levels in patients with extrahepatic biliary atresia and neonatal hepatitis during the first 10 days of life

1985 • 12 citations

Functional Outcomes of Pediatric Liver Transplantation

2003 • 12 citations

Serum Bile Acid Patterns Determined by an Enzymatic Method and High-Performance Liquid Chromatography in Young Infants with Cholestasis

1984 • 10 citations

Bile Acid Metabolism in Extrahepatic Biliary Atresia

2006 • 8 citations

Unconjugated, Glycine‐conjugated, Taurine‐conjugated Bile Acid Nonsulfates and Sulfates in Urine of Young Infants with Cholestasis

1984 • 8 citations

CFC1 Gene Mutation and Biliary Atresia With Polysplenia Syndrome

2002 • 5 citations

Body Composition of Children Aged 1 to 12 years with Biliary Atresia or Alagille Syndrome

2005 • 4 citations

P0210 STOOL COLOR CARDS SCREENING FOR INFANTS AGED ONE MONTH

2004 • 1 citations

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Screening and outcomes in biliary atresia: Summary of a National Institutes of Health… (2007) – Hepatology | Metascience Observatory Explorer