Structure of the asparagine-linked sugar chains of porcine kidney and human urine cerebroside sulfate activator protein

The Metabolic and Molecular Bases of Inherited Disease

1995 • 12,086 citations

ASSEMBLY OF ASPARAGINE-LINKED OLIGOSACCHARIDES

1985 • 4,790 citations

A systematic nomenclature for carbohydrate fragmentations in FAB-MS/MS spectra of glycoconjugates

1988 • 2,610 citations

Delayed extraction matrix‐assisted laser desorption time‐of‐flight mass spectrometry

1995 • 488 citations

Mass Resolution Improvement by Incorporation of Pulsed Ion Extraction in a Matrix-Assisted Laser Desorption/Ionization Linear Time-of-Flight Mass Spectrometer

1995 • 369 citations

Saposin proteins: structure, function, and role in human lysosomal storage disorders

1991 • 328 citations

Improving the resolution of matrix‐assisted laser desorption/ionization time‐of‐flight mass spectrometry by exploiting the correlation between ion position and velocity

1994 • 164 citations

A simple method for dialysis of small-volume samples

1980 • 163 citations

The Activator of Cerebroside Sulphatase. Purification from Human Liver and Identification as a Protein

1975 • 135 citations

Ion exchange and purification of carbohydrates on a Nafion® membrane as a new sample pretreatment for matrix‐assisted laser desorption/ionization mass spectrometry

1995 • 120 citations

Characterization of a mutation in a family with saposin B deficiency: a glycosylation site defect.

1990 • 116 citations

High-Sensitivity Detection and Postsource Decay of 2-Aminopyridine-Derivatized Oligosaccharides with Matrix-Assisted Laser Desorption/Ionization Mass Spectrometry

1997 • 103 citations

Analysis of Carbohydrate Heterogeneity in a Glycoprotein Using Liquid Chromatography/Mass Spectrometry and Liquid Chromatography with Tandem Mass Spectrometry

1999 • 92 citations

Characterization of a nonspecific activator protein for the enzymatic hydrolysis of glycolipids.

1988 • 92 citations

Glycosphingolipid specifity of the human sulfatide activator protein

1991 • 82 citations

Sensitive detection and structural characterization of trimethyl(p‐aminophenyl)‐ammonium‐derivatized oligosaccharides by electrospray ionization–mass spectrometry and tandem mass spectrometry

1995 • 75 citations

Biosynthesis of the sulfatide/GM1 activator protein (SAP-1) in control and mutant cultured skin fibroblasts

1986 • 73 citations

Fast atom bombardment mass spectrometric strategies for characterizing carbohydrate-containing biopolymers

1988 • 69 citations

Detection of a point mutation in sphingolipid activator protein-1 mRNA in patients with a variant form of metachromatic leukodystrophy

1990 • 63 citations

A Conserved Disulfide Motif in Human Tear Lipocalins Influences Ligand Binding

1998 • 61 citations

Requirement of an activator for the hydrolysis of sphingoglycolipids by glycosidases of human liver

1974 • 60 citations

The complete amino‐acid sequences of human ganglioside GM2 activator protein and cerebroside sulfate activator protein

1990 • 58 citations

The Effect of Carbohydrate Removal on Stability and Activity of Saposin B

1993 • 42 citations

Drop dialysis: Time course of salt and protein exchange

1988 • 42 citations

A non‐glycosylated and functionally deficient mutant (N215H) of the sphingolipid activator protein B (SAP‐B) in a novel case of metachromatic leukodystrophy (MLD)

2000 • 37 citations

An Asn > Lys substitution in saposin B involving a conserved amino acidic residue and leading to the loss of the single N-glycosylation site in a patient with metachromatic leukodystrophy and normal arylsulphatase A activity

1999 • 33 citations

STUDIES ON THE SPHINGOLIPID ACTIVATOR PROTEIN FOR THE ENZYMATIC HYDROLYSIS OF GM1 GANGLIOSIDE AND SULFATIDE

1984 • 31 citations

The cerebroside sulfate activator from pig kidney: Purification and molecular structure

1992 • 20 citations

Porcine cerebroside sulfate activator: Further structural characterization and disulfide identification

1993 • 17 citations

Characteristics of asparagine-linked sugar chains of sphingolipid activator protein 1 purified from normal human liver and GM1 gangliosidosis (type 1) liver

1990 • 16 citations

Complete Amino-Acid Sequence of the Naturally Occurring A₂Activator Protein for Enzymic Sphingomyelin Degradation: Identity to the Sulfatide Activator Protein (SAP-1)

1988 • 15 citations

Cerebroside sulfate activator protein (Saposin B): chromatographic and electrospray mass spectrometric properties

1999 • 13 citations

The Cerebroside Sulfate Activator(Saposin B, SAP-1): A Many Faceted Protein.

1995 • 12 citations

Preparation of the Cerebroside Sulfate Activator (CSAct or Saposin B) from Human Urine

1999 • 7 citations