Isolation and characterization of a precursor form of lysosomal α‐glucosidase from human urine

Electrophoretic transfer of proteins from polyacrylamide gels to nitrocellulose sheets: procedure and some applications.

1979 • 54,907 citations

Methods of Enzymatic Analysis

1975 • 20,446 citations

Biosynthesis of lysosomal enzymes in fibroblasts. Synthesis as precursors of higher molecular weight.

1980 • 809 citations

Isozymes. Current Topics in Biological and Medical Research

1982 • 444 citations

Biosynthesis of lysosomal enzymes in fibroblasts. Phosphorylation of mannose residues.

1980 • 404 citations

The Phosphomannosyl Recognition System for Intracellular and Intercellular Transport of Lysosomal Enzymes

1982 • 379 citations

Recognition and receptor-mediated uptake of a lysosomal enzyme, α-l-iduronidase, by cultured human fibroblasts

1977 • 354 citations

Lysosomes and lysosomal storage diseases

1981 • 315 citations

Biosynthetic intermediates of beta-glucuronidase contain high mannose oligosaccharides with blocked phosphate residues.

1980 • 225 citations

Enzymatic identification of mannose 6-phosphate on the recognition marker for receptor-mediated pinocytosis of beta-glucuronidase by human fibroblasts.

1979 • 212 citations

Lysosomal Enzyme Precursors in Human Fibroblasts. Activation of Cathepsin D Precursor in vitro and Activity of beta-Hexosaminidase A Precursor towards Ganglioside GM2

1982 • 163 citations

G1 Ganglioside β-Galactosidase A

1974 • 158 citations

l-Glutamate UV-Assay with Gutamate Dehydrogenase and NAD

1974 • 125 citations

Invitro correction of deficient human fibroblasts by β-glucuronidase from different human sources

1974 • 101 citations

Maturation of alpha-L-iduronidase in cultured human fibroblasts.

1981 • 97 citations

Coordinacy of lysosomal enzyme excretion in human urine.

1978 • 87 citations

Lysosomal enzyme oligosaccharide phosphorylation in mouse lymphoma cells: specificity and kinetics of binding to the mannose 6-phosphate receptor in vivo

1982 • 82 citations

Enhanced Breakdown of Arylsulfatase A in Multiple Sulfatase Deficiency

1982 • 76 citations

Studies on the Pathogenetic Mechanism of I-Cell Disease in Cultured Fibroblasts

1974 • 75 citations

Quantitative Aspects of Pinocytosis and the Intracellular Fate of N-acetyl-α-D-glucosaminidase in Sanfilippo B Fibroblasts

1974 • 73 citations

Synthesis and Processing of Arylsulfatase A in Human Skin Fibroblasts

1982 • 65 citations

The relationship of α-l-iduronidase and Hurler corrective factor

1976 • 49 citations

Purification of an acid α-glucosidase by dextran-gel filtration

1967 • 48 citations

Biosynthesis of acid α‐glucosidase in late‐onset forms of glycogenosis type II (Pompe's disease)

1982 • 44 citations

The molecular heterogeneity of purified human liver lysosomal α-Glucosidase (acid α-Glucosidase)

1978 • 42 citations

Monoclonal antibodies against human acid α-glucosidase

1981 • 41 citations

Use of immobilized antibodies in investigating acid α-glucosidase in urine in relation to Pompe's disease

1979 • 37 citations

Purification and characterization of I-cell disease alpha-L-fucosidase.

1980 • 33 citations

Adult forms of glycogenosis type II

1982 • 31 citations

Use of a monoclonal antibody to distinguish between precursor and mature forms of human lysosomal α‐glucosidase

1984 • 28 citations

Inactivation by chloroquine of α-galactosidase in cultured human skin fibroblasts

1981 • 23 citations

Mucolipidosis III β-N-acetyl-<scp>d</scp>-hexosaminidase A. Purification and properties

1982 • 17 citations

A study of highly purified mucolipidosis III urinary N-acetyl-β-D-hexosaminidase B

1982 • 8 citations