Hepatic and Muscular Presentations of Carnitine Palmitoyl Transferase Deficiency: Two Distinct Entities

PROTEIN MEASUREMENT WITH THE FOLIN PHENOL REAGENT

1951 • 319,299 citations

Regulation of Hepatic Fatty Acid Oxidation and Ketone Body Production

1980 • 1,430 citations

Carnitine palmitoyltransferase I. The site of inhibition of hepatic fatty acid oxidation by malonyl-CoA.

1978 • 586 citations

Fasting hypoglycemia resulting from hepatic carnitine palmitoyl transferase deficiency

1981 • 173 citations

Carnitine metabolism and deficiency syndromes.

1983 • 159 citations

Regulatory properties of a mutant carnitine palmitoyltransferase in human skeletal muscle

1985 • 89 citations

Mechanism of carnitine acylcarnitine translocase-catalyzed import of acylcarnitines into mitochondria.

1984 • 86 citations

Characterization of the Mitochondrial Carnitine Palmitoyltransferase Enzyme System

1987 • 68 citations

Heterogeneity of carnitine-palmitoyltransferase deficiency

1981 • 45 citations

Effects of thyroidectomy and starvation on the activity and properties of hepatic carnitine palmitoyltransferase

1982 • 45 citations

Carnitine palmitoyltransferase: characterization of a labile detergent-extracted malonyl-CoA-sensitive enzyme from rat liver mitochondria

1987 • 35 citations