Experimental animal model for mucopolysaccharidosis: suramin-induced glycosaminoglycan and sphingolipid accumulation in the rat.

A modified uronic acid carbazole reaction

1962 • 6,191 citations

The Metabolic Basis of Inherited Disease

1979 • 2,083 citations

CHROMATOGRAPHlC SEPARATION OF HUMAN BRAIN GANGLIOSIDES*

1963 • 1,644 citations

Lysosomes and storage diseases

1973 • 745 citations

Inherited Disorders of Lysosomal Metabolism

1975 • 322 citations

A rapid and micro method for separation of acidic glycosaminoglycans by two-dimensional electrophoresis

1972 • 299 citations

The Defect in the Hunter Syndrome: Deficiency of Sulfoiduronate Sulfatase

1973 • 231 citations

Advances in experimental medicine and biology

1984 • 221 citations

The Molecular basis of neuropathology

1981 • 217 citations

[46] Enzymic diagnosis of the genetic mucopolysaccharide storage disorders

1978 • 204 citations

Sanfilippo Syndrome: Profound Deficiency of Alpha-Acetylglucosaminidase Activity in Organs and Skin Fibroblasts from Type-B Patients

1972 • 160 citations

Structure of Dermatan Sulfate

1967 • 133 citations

The mucopolysaccharidoses (a review).

1976 • 129 citations

Degradation of mucopolysaccharides by hepatic lysosomes

1966 • 89 citations

Methods in Carbohydrate Chemistry

1976 • 82 citations

NEUROCHEMISTRY OF THE MUCOPOLYSACCHARIDOSES: BRAIN LIPIDS AND LYSOSOMAL ENZYMES IN PATIENTS WITH FOUR TYPES OF MUCOPOLYSACCHARIDOSIS AND IN NORMAL CONTROLS

1978 • 77 citations

Determination of molecular weight distribution of acid mucopolysaccharides by Sephadex gel filtration

1969 • 77 citations

A micromethod for the determination of acid mucopolysaccharides in vascular tissue

1967 • 57 citations

Muscle, nerve and brain degeneration

1980 • 53 citations

Sphingolipid hydrolases in brain tissue of patients with generalized gangliodosis

1970 • 48 citations

NEUROCHEMISTRY OF THE MUCOPOLYSACCHARIDOSES: BRAIN GLYCOSAMINOGLYCANS IN NORMALS AND FOUR TYPES OF MUCOPOLYSACCHARIDOSES

1976 • 44 citations

Comparative Biochemistry and Drug Design for Infectious Disease

1979 • 44 citations

Handbook of Neurochemistry

1973 • 30 citations

Response of sphingolipid hydrolases in spleen and liver to increased erythrocytorhexis

1967 • 26 citations

Membranous neuronal and neuroglial inclusions produced by intracerebral injection of suramin

1978 • 15 citations

Lysosomes and congenital malformations

1969 • 10 citations

[11] Radioactive substrates for iduronate sulfatase and α-l-iduronidase

1978 • 9 citations

[Effect of suramine on perinatal and postnatal survival in mice].

1973 • 1 citations