Very long‐chain acyl coenzyme A dehydrogenase deficiency presenting with exercise‐induced myoglobinuria

[2] Citrate synthase from rat liver

1969 • 435 citations

Fuel Homeostasis in Exercise

1975 • 403 citations

THE QUANTITATIVELY MINOR ROLE OF CARBOHYDRATE IN OXIDATIVE METABOLISM BY SKELETAL MUSCLE IN INTACT MAN IN THE BASAL STATE. MEASUREMENTS OF OXYGEN AND GLUCOSE UPTAKE AND CARBON DIOXIDE AND LACTATE PRODUCTION IN THE FOREARM 12

1956 • 393 citations

Novel fatty acid beta-oxidation enzymes in rat liver mitochondria. I. Purification and properties of very-long-chain acyl-coenzyme A dehydrogenase.

1992 • 245 citations

An acyl-coenzyme a dehydrogenase assay utilizing the ferricenium ion

1990 • 217 citations

A Novel Disease with Deficiency of Mitochondrial Very-Long-Chain Acyl-CoA Dehydrogenase

1993 • 150 citations

Very long chain acyl-CoA dehydrogenase deficiency: identification of a new inborn error of mitochondrial fatty acid oxidation in fibroblasts

1993 • 122 citations

Quantitation of acyl-CoA and acylcarnitine esters accumulated during abnormal mitochondrial fatty acid oxidation.

1991 • 89 citations

Measurement of the activity of individual respiratory chain complexes in isolated fibroblast mitochondria

1992 • 27 citations

A Simple Spectrophotometric Assay for Long-Chain Acyl-CoA Dehydrogenase Activity Measurements in Human Skin Fibroblasts

1993 • 16 citations

Measurement of acyl‐CoA dehydrogenase activity in cultured skin fibroblasts and blood platelets

1991 • 6 citations