Alloisoleucine Formation in Maple Syrup Urine Disease: Isotopic Evidence for the Mechanism

Rapid Gas Chromatographic Separation of Amino Acid Enantiomers with a Novel Chiral Stationary Phase

1977 • 542 citations

Determination of amino acid profiles in biological samples by gas chromatography

1974 • 252 citations

MAPLE SYRUP URINE DISEASE, WITH PARTICULAR REFERENCE TO DIETOTHERAPY

1964 • 229 citations

Determination of stable isotopic enrichment in individual plasma amino acids by chemical ionization mass spectrometry

1979 • 149 citations

A NEW FINDING IN MAPLE-SYRUP-URINE DISEASE

1962 • 33 citations

Glucose and Alanine Metabolism in Children with Maple Syrup Urine Disease

1978 • 29 citations

The configuration of the alloisoleucine present in maple syrup urine disease plasma

1970 • 18 citations