Clinical and neuropathologic variation in neuronal intermediate filament inclusion disease

Frontotemporal lobar degeneration

1998 • 4,937 citations

El escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis

1994 • 2,090 citations

Corticobasal degeneration and its relationship to progressive supranuclear palsy and frontotemporal dementia

2003 • 517 citations

Two-stage expression of neurofilament polypeptides during rat neurogenesis with early establishment of adult phosphorylation patterns

1987 • 503 citations

Monoclonal antibodies distinguish several differentially phosphorylated states of the two largest rat neurofilament subunits (NF-H and NF-M) and demonstrate their existence in the normal nervous system of adult rats

1987 • 490 citations

Frontal lobe dementia and motor neuron disease.

1990 • 437 citations

Neuronal Intermediate Filaments

1996 • 435 citations

Novel antibodies to synuclein show abundant striatal pathology in Lewy body diseases

2002 • 325 citations

New ubiquitin-positive intraneuronal inclusions in the extra-motor cortices in patients with amyotrophic lateral sclerosis

1991 • 227 citations

Phosphorylation protects neurofilaments against proteolysis

1987 • 199 citations

Phosphorylation of Neurofilaments Is Altered in Amyotrophic Lateral Sclerosis

1988 • 198 citations

Neurofilaments and neurological disease

2003 • 180 citations

Phosphate dependent and independent neurofilament epitopes in the axonal swellings of patients with motor neuron disease and controls.

1987 • 178 citations

Neurofilament inclusion body disease: a new proteinopathy?

2003 • 171 citations

Epitope map of neurofilament protein domains in cortical and peripheral nervous system Lewy bodies.

1991 • 161 citations

Familial frontotemporal dementia with ubiquitin-positive, tau-negative inclusions

2000 • 135 citations

Alzheimer disease tangles share immunological similarities with multiphosphorylation repeats in the two large neurofilament proteins.

1988 • 125 citations

Expression of the gene for the neuronal intermediate filament protein α‐internexin coincides with the onset of neuronal differentiation in the developing rat nervous system

1994 • 125 citations

α-Internexin Is Present in the Pathological Inclusions of Neuronal Intermediate Filament Inclusion Disease

2004 • 117 citations

Overexpression of α-Internexin Causes Abnormal Neurofilamentous Accumulations and Motor Coordination Deficits in Transgenic Mice

1999 • 96 citations

CYTOSKELETAL ABNORMALITIES IN MOTOR NEURON DISEASE

1989 • 94 citations

Frontotemporal and motor neurone degeneration with neurofilament inclusion bodies: additional evidence for overlap between FTD and ALS

2003 • 85 citations

Comparative epitope analysis of neuronal cytoskeletal proteins in Alzheimer's disease senile plaque neurites and neuropil threads.

1991 • 82 citations

Patients with a novel neurofilamentopathy: dementia with neurofilament inclusions

2003 • 79 citations

Phosphorylation state of the native high‐molecular‐weight neurofilament subunit protein from cervical spinal cord in sporadic amyotrophic lateral sclerosis

2001 • 75 citations

Structure of the gene for the neuronal intermediate filament protein alpha-internexin and functional analysis of its promoter.

1991 • 62 citations

Relative abundance of tau and neurofilament epitopes in hippocampal neurofibrillary tangles.

1990 • 60 citations

?-Internexin aggregates are abundant in neuronal intermediate filament inclusion disease (NIFID) but rare in other neurodegenerative diseases

2004 • 55 citations

Neurofilament inclusion body disease with early onset frontotemporal dementia and primary lateral sclerosis.

2004 • 44 citations

Roles of head and tail domains in α-internexin’s self-assembly and coassembly with the neurofilament triplet proteins

1998 • 42 citations

Utilizing the Peptidyl-Prolyl Cis-Trans Isomerase Pin1 as a Probe of Its Phosphorylated Target Proteins: Examples of Binding to Nuclear Proteins in a Human Kidney Cell Line and to Tau in Alzheimer's Diseased Brain

2001 • 35 citations

Aggregation of Intermediate Filaments by 2,5-Hexanedione: Comparison of Effects on Neurofilaments, GFAP-Filaments and Vimentin-Filaments in Dissociated Cultures of Mouse Spinal Cord--Dorsal Root Ganglia

1988 • 27 citations

Neuropathology of amyotrophic lateral sclerosis with extra-motor system degeneration: Characteristics and differences in the molecular pathology between ALS with dementia and Guamanian ALS

2000 • 23 citations

Neurofilament-Rich Intraneuronal Inclusions Exacerbate Neurodegenerative Sequelae of Brain Trauma in NFH/LacZ Transgenic Mice

2000 • 20 citations

A case of Pick's disease with unusual neuronal inclusions

1994 • 15 citations