Urinary excretion of dicarboxylic acids from patients with the zellweger syndrome Importance of peroxisomes in β-oxidation of dicarboxylic acids

Enzymic determination of <scp>d</scp>(−)-β-hydroxybutyric acid and acetoacetic acid in blood

1962 • 1,407 citations

Peroxisomal and Mitochondrial Defects in the Cerebro-Hepato-Renal Syndrome

1973 • 777 citations

Cerebro-hepato-renal syndrome of Zellweger

1975 • 246 citations

Jamaican Vomiting Sickness

1976 • 208 citations

Defects of Bile Acid Synthesis in Zellweger's Syndrome

1979 • 171 citations

The mechanism of arrest of neuronal migration in the Zellweger malformation: An hypothesis based upon cytoarchitectonic analysis

1978 • 171 citations

The occurrence of adipic and suberic acid in urine from ketotic patients

1972 • 162 citations

Suberylglycine excretion in the urine from a patient with dicarboxylic aciduria

1976 • 134 citations

A Novel mechanism for inhibition of β‐oxidation by methylenecyclopropylacetyl‐CoA, a metabolite of hypoglycin

1975 • 91 citations

C27 Bile Acids in Infants with Coprostanic Acidemia and Occurrence of a 3alpha,7alpha,12alpha-Trihydroxy-5beta-C29 Dicarboxylic Bile Acid as a Major Component in Their Serum

1979 • 90 citations

Cyanide-insensitive and clofibrate enhanced β -oxidation of dodecanedioic acid in rat liver an indication of peroxisomal β-oxidation of N-dicarboxylic acids

1982 • 77 citations

Liver in the cerebro-hepato-renal syndrome: Defective bile acid synthesis and abnormal mitochondria

1980 • 74 citations

Biochemical Studies in the Liver and Muscle of Patients with Zellweger Syndrome

1983 • 73 citations

In vitro enzymic omega oxidation of medium-chain fatty acids in mammalian tissue

1968 • 64 citations

Relative contributions of α-, β-, and ω-oxidative pathways to in vitro fatty acid oxidation in rat liver

1968 • 57 citations

C6–C10-dicarboxylic aciduria in starved, fat-fed and diabetic rats receiving decanoic acid or medium-chain triacylglycerol an in vivo measure of the rate of β-oxidation of fatty acids

1981 • 54 citations

The occurrence of C6–C10-dicarboxylic acids in urine from patients and rats treated with dipropylacetate

1980 • 52 citations

Intermittent non‐ketotic dicarboxylic aciduria in two siblings with hypoglycaemia: An apparent defect in β‐oxidation of fatty acids

1979 • 52 citations

Inhibition of electron transport and coupled phosphorylation in liver mitochondria by cholanic (bile) acids and their conjugates

1965 • 52 citations

On the quantitative importance of omega-oxidation of fatty acids.

1978 • 51 citations

Dicarboxylic aciduria: The response to fasting

1979 • 48 citations

The biological origin of ketotic dicarboxylic aciduria

1982 • 46 citations

Exercise-induced asthma after walking, running and cycling

1982 • 40 citations

Aliphatic C6−C14 dicarboxylic acids in urine from an infant with fatal congenital lactic acidosis

1972 • 33 citations

Specific and sensitive method for the determination of C6C10 dicarboxylic acids in serum and urine by selected ion monitoring

1979 • 20 citations