Allosteric inhibition of human lymphoblast and purified porphobilinogen deaminase by protoporphyrinogen and coproporphyrinogen. A possible mechanism for the acute attack of variegate porphyria.

Release of Infectious Epstein-Barr Virus by Transformed Marmoset Leukocytes

1973 • 960 citations

Statistical Methods in Biology.

1995 • 292 citations

Physical Biochemistry

1970 • 287 citations

The Enzymatic Defect in Variegate Porphyria

1980 • 160 citations

Evidence for a dipyrromethane cofactor at the catalytic site of E. coli porphobilinogen deaminase

1987 • 143 citations

Purification and properties of uroporphyrinogen I synthase from human erythrocytes. Identification of stable enzyme-substrate intermediates.

1980 • 133 citations

Decreased Red Cell Uroporphyrinogen I Synthetase Activity in Intermittent Acute Porphyria

1972 • 131 citations

The inherited enzymatic defect in porphyria variegata

1981 • 127 citations

A Microassay for Uroporphyrinogen I Synthase, One of Three Abnormal Enzyme Activities in Acute Intermittent Porphyria, and its Application to the Study of the Genetics of this Disease

1974 • 98 citations

The clinical and biochemical features of variegate porphyria: An analysis of 300 cases studied at Groote Schuur Hospital, Cape Town

1980 • 88 citations

THE PRIMARY ENZYME DEFECT IN HEREDITARY COPROPORPHYRIA

1976 • 88 citations

Studies in Porphyria

1978 • 77 citations

Decreased lymphocyte coproporphyrinogen III oxidase activity in hereditary coproporphyria

1977 • 70 citations

The diagnostic value of blood plasma porphyrin methyl ester profiles produced by quantitative TLC

1978 • 61 citations

Quantitation of red cell porphyrins by fluorescence scanning after thin-layer chromatography

1978 • 57 citations

Porphyrin biosynthesis

1969 • 52 citations

A fluorometric assay for measurement of protoporphyrinogen oxidase activity in mammalian tissue

1980 • 51 citations

Modified erythrocyte uroporphyrinogen I synthase assay, and its clinical interpretation.

1978 • 51 citations

Protoporphyrinogen oxidase and porphobilinogen deaminase in variegate porphyria

1986 • 46 citations

Porphyria Cutanea Tarda

1982 • 43 citations

Porphobilinogen Deaminase: Methods and Principles of the Enzymatic Assay

1982 • 42 citations

Porphyria cutanea tarda

1970 • 34 citations

Assay for erythrocyte uroporphyrinogen I synthase activity, with porphobilinogen as substrate.

1980 • 34 citations

Biosynthesis of the Pigments of Life

1988 • 29 citations

Is Porphobilinogen Deaminase Activity a Secondary Control Mechanism in Haem Biosynthesis in Humans?

1977 • 28 citations

Enzyme catalysis and regulation

1983 • 27 citations

Protoporphyrinogen oxidase and ferrochelatase in porphyria variegata

1983 • 23 citations

Ferriprotoporphyrin IX Oxygen Activation/Insertion Reactions: The Nature of the Interaction between Ferriprotoporphyrin IX and Aniline (Substrate)

1986 • 16 citations

Oxygen activation and tetrapyrroles.

1981 • 13 citations

Porphyria--the UCT experience.

1987 • 13 citations

Porphyrin biosynthesis in soybean callus. V. The porphobilinogen deaminase-uroporphyrinogen cosynthetase system. Kinetic studies

1970 • 11 citations

Human red cell porphobilinogen deaminase. a simpler method of purification and some unusual properties

1985 • 8 citations

Intracellular activity of HPRT_{Cape Town}: Purine uptake and growth of cultured cells in selective media

1985 • 6 citations

Purification of human erythrocyte porphobilinogen deaminase.

1991 • 1 citations