MRI evidence that docosahexaenoic acid ethyl ester improves myelination in generalized peroxisomal disorders

Biochemical and functional effects of prenatal and postnatal omega 3 fatty acid deficiency on retina and brain in rhesus monkeys.

1986 • 922 citations

Peroxisomal and Mitochondrial Defects in the Cerebro-Hepato-Renal Syndrome

1973 • 777 citations

The metabolism of 7,10,13,16,19-docosapentaenoic acid to 4,7,10,13,16,19-docosahexaenoic acid in rat liver is independent of a 4-desaturase.

1991 • 660 citations

Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.

1984 • 344 citations

Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome)

1983 • 340 citations

Alterations in the Fatty Acid Composition of Rat Brain Cells (Neurons, Astrocytes, and Oligodendrocytes) and of Subcellular Fractions (Myelin and Synaptosomes) Induced by a Diet Devoid of n‐3 Fatty Acids

1984 • 321 citations

Defects of Bile Acid Synthesis in Zellweger's Syndrome

1979 • 171 citations

THE ISOLATION AND CHARACTERIZATION OF A PLASMA MEMBRANE AND A MYELIN FRACTION DERIVED FROM OLIGODENDROGLIA OF CALF BRAIN

1975 • 158 citations

3-Hydroxy-3-methylglutaryl-coenzyme A reductase is present in peroxisomes in normal rat liver cells.

1985 • 158 citations

Magnetic Resonance of Myelin, Myelination, and Myelin Disorders

1995 • 124 citations

A comparison of pyrrolidide and picolinyl ester derivatives for the identification of fatty acids in natural samples by gas chromatography‐mass spectrometry

1986 • 108 citations

Severe deficiency of docosahexaenoic acid in peroxisomal disorders

1990 • 100 citations

Docosahexaenoic acid therapy in docosahexaenoic acid‐deficient patients with disorders of peroxisomal biogenesis

1996 • 71 citations

Polyunsaturated fatty acid changes suggesting a new enzymatic defect in Zellweger Syndrome

1989 • 67 citations

Docosahexaenoic acid–A new therapeutic approach to peroxisomal‐disorder patients

1993 • 64 citations

Blood polyunsaturated fatty acids in patients with peroxisomal disorders. A multicenter study

1994 • 54 citations

Liver Peroxisomes and Bile Acid Formation

1987 • 18 citations