Amyotrophic lateral sclerosis with dementia: an autopsy case showing many Bunina bodies, tau-positive neuronal and astrocytic plaque-like pathologies, and pallido-nigral degeneration

Neuropathological stageing of Alzheimer-related changes

1991 • 14,533 citations

Penetrance of the Fragile X–Associated Tremor/Ataxia Syndrome in a Premutation Carrier Population

2004 • 631 citations

The central nervous system in motor neurone disease

1970 • 473 citations

Alzheimer's Neurofibrillary Changes

1962 • 396 citations

The fragile X syndrome.

1998 • 266 citations

New ubiquitin-positive intraneuronal inclusions in the extra-motor cortices in patients with amyotrophic lateral sclerosis

1991 • 227 citations

Pathological inclusion bodies in tauopathies contain distinct complements of tau with three or four microtubule‐binding repeat domains as demonstrated by new specific monoclonal antibodies

2003 • 204 citations

Neuropathology with Clinical Correlations of Sporadic Amyotrophic Lateral Sclerosis: 102 Autopsy Cases Examined Between 1962 and 2000

2003 • 201 citations

Trinucleotide repeat expansion in neurological disease

1994 • 185 citations

Bunina bodies in amyotrophic lateral sclerosis immunostained with rabbit anti-cystatin C serum

1993 • 126 citations

Immunocytochemical and ultrastructural studies of lower motor neurons in amyotrophic lateral sclerosis

1990 • 125 citations

Initial diagnoses given to persons with the fragile X associated tremor/ataxia syndrome (FXTAS)

2005 • 114 citations

Thorn-shaped astrocytes: possibly secondarily induced tau-positive glial fibrillary tangles

1995 • 113 citations

Familial amyotrophic lateral sclerosis and parkinsonism‐dementia complex of the Kii peninsula of Japan: Clinical and neuropathological study and tau analysis

2001 • 111 citations

The Fragile-X Syndrome

1992 • 107 citations

Amyotrophic Lateral Sclerosis

1967 • 89 citations

Familial amyotrophic lateral sclerosis with a point mutation of SOD-1: intrafamilial heterogeneity of disease duration associated with neurofibrillary tangles.

1995 • 86 citations

Microtubule-associated tau protein positive neuronal and glial inclusions in ALS

2003 • 81 citations

Amyotrophic lateral sclerosis of Guam: the nature of the neuropathological findings

1994 • 60 citations

Rapidly progressive aphasia and motor neuron disease: a clinical, radiological, and pathological study of an autopsy case with circumscribed lobar atrophy

2000 • 59 citations

Alzheimer disease pathology in amyotrophic lateral sclerosis

2004 • 57 citations

Ubiquitin-immunoreactive filamentous inclusions in anterior horn cells of Guamanian and non-Guamanian amyotrophic lateral sclerosis

1990 • 52 citations

Different immunoreactivities of the microtubule-binding region of tau and its molecular basis in brains from patients with Alzheimer's disease, Pick's disease, progressive supranuclear palsy and corticobasal degeneration

2003 • 52 citations

Spinal cord neurofibrillary tangles of Guamanian amyotrophic lateral sclerosis and parkinsonism‐dementia complex

1990 • 51 citations

Substantia Nigra in Progressive Supranuclear Palsy, Corticobasal Degeneration, and Parkinsonism-Dementia Complex of Guam: Specific Pathological Features

2001 • 46 citations

Temporal Lobe Lesions in Amyotrophic Lateral Sclerosis with or without Dementia: A Neuropathological Study

1993 • 46 citations

Luyso-pallido-nigral atrophy and amyotrophic lateral sclerosis

1985 • 45 citations

Cognitive dysfunction in patients with amyotrophic lateral sclerosis is associated with spherical or crescent-shaped ubiquitinated intraneuronal inclusions in the parahippocampal gyrus and amygdala, but not in the neostriatum

2001 • 41 citations

NACP/α-synuclein immunoreactivity in diffuse neurofibrillary tangles with calcification (DNTC)

2002 • 40 citations

Sporadic amyotrophic lateral sclerosis with circumscribed temporal atrophy: A report of an autopsy case without dementia and with ubiquitinated intraneuronal inclusions

2002 • 39 citations

Microglial tau undergoes phosphorylation‐independent modification after ischemia

2003 • 37 citations

Constant involvement of the Betz cells and pyramidal tract in amyotrophic lateral sclerosis with dementia: a clinicopathological study of eight autopsy cases

2002 • 36 citations

Atypical amyotrophic lateral sclerosis with dementia mimicking frontal Pick's disease: a report of an autopsy case with a clinical course of 15 years

2001 • 35 citations

Sporadic four-repeat tauopathy with frontotemporal degeneration, parkinsonism and motor neuron disease

2005 • 33 citations

Sporadic amyotrophic lateral sclerosis with multiple system degeneration: a report of an autopsy case without respirator administration

1999 • 27 citations

Frontotemporal dementia, motor neuron disease and tauopathy: clinical and neuropathological study in a family

2005 • 23 citations

Sporadic amyotrophic lateral sclerosis of long duration mimicking spinal progressive muscular atrophy exists: Additional autopsy case with a clinical course of 19 years

2004 • 22 citations

Gallyas- and tau-positive glial structures in motor neuron disease with dementia.

1999 • 22 citations

Amyotrophic lateral sclerosis in a patient with fragile X syndrome

1990 • 20 citations

Motor neuron disease with neurofibrillary tangles in a non-Guamanian patient

1995 • 17 citations

Increased expression of neuronal cyclooxygenase-2 in the hippocampus in amyotrophic lateral sclerosis both with and without dementia

2004 • 17 citations

Motor neuron disease with involvement of the pallido-luysio-nigral system and mesencephalic tegmentum.

1995 • 16 citations

“Forme fruste” of amyotrophic lateral sclerosis with dementia: A report of five autopsy cases without dementia and with ubiquitinated intraneuronal inclusions

2005 • 14 citations

Neurofibrillary degeneration in a case of quadriplegia and myoclonic movement

1979 • 13 citations

Familial amyotrophic lateral sclerosis with onset in bulbar sign, benign clinical course, and Bunina bodies: a clinical, genetic, and pathological study of a Japanese family

2000 • 13 citations