Back to search

Activation of membrane-bound glucosylceramide: beta-glucosidase in fibroblasts cultured from normal and glucosylceramidotic human skin.

Data up to Jan 2025

Published1979
Citations38
References21

Total Citations Per Year

Abstract

References (21)

Quantitive estimation of sialic acids

1957 • 2,782 citations

Metabolism of glucocerebrosides II. Evidence of an enzymatic deficiency in Gaucher's disease

1965 • 800 citations

A Deficiency of Glucocerebrosidase in Gaucher's Disease

1965 • 248 citations

Differentiation of β-glucocerebrosidase from β-glucosidase in human tissues using sodium taurocholate

1976 • 200 citations

Isolation and Characterization of Glucocerebrosidase from Human Placental Tissue

1973 • 169 citations

Purification and properties of a heat-stable glucocerebrosidase activating factor from control and Gaucher spleen.

1977 • 118 citations

C20-sphingosine as a determining factor in aggregation of gangliosides.

1976 • 108 citations

Glycosphingolipids in Cultured Human Skin Fibroblasts

1972 • 102 citations

Adult Gaucher's disease: kindred studies and demonstration of a deficiency of acid beta-glucosidase in cultured fibroblasts.

1972 • 94 citations

Glucocerebrosidase: reconstitution from macromolecular components depends on acidic phospholipids (Short Communication)

1973 • 71 citations

Solubilization of glucocerebrosidase from human placenta and demonstration of a phospholipid requirement for its catalytic activity

1976 • 66 citations

Identity of ‘acid’ β-glucosidase and glucocerebrosidase in human spleen

1973 • 65 citations

Monogalactosyl and digalactosyl diglycerides from heterotrophic, hetero-autotrophic, and photobiotic Euglena gracilis

1966 • 61 citations

Enzyme replacement therapy in Gaucher's disease: a rapid, high-yield method for purification of glucocerebrosidase.

1976 • 47 citations

beta-Glucoside hydrolase activity of normal and glucosylceramidotic cultured human skin fibroblasts.

1977 • 40 citations

β-Glucosidase activities in human tissues findings in Gaucher's disease

1970 • 38 citations

Ribonucleic acid synthesis by Escherichia coli C3000/L after infection by the ribonucleic acid coliphage ZIK/1, and properties of coliphage-ZIK/1 ribonucleic acid

1965 • 34 citations

Rapid partial purification of placental glucocerebroside β-glucosidase and its entrapment in liposomes

1977 • 32 citations

Metabolism of glucosyl [13H]ceramide by human skin fibroblasts from normal and glucosylceramidotic subjects.

1975 • 31 citations

Gaucher's disease, chronic adult type: a comparative study of glucocerebroside and methylumbelliferyl-glucopyranoside cleaving potency in leukocytes.

1974 • 21 citations

4-Methylumbelliferyl-β-glucosidase in cultured human fibroblasts from controls and patients with gaucher's disease

1973 • 15 citations

Cited By (0)

Loading...
Activation of membrane-bound glucosylceramide: beta-glucosidase in fibroblasts cultured… (1979) – Journal of Biological Chemistry | Metascience Observatory Explorer