Synthesis and processing of sphingolipid activator protein-2 (SAP-2) in cultured human fibroblasts.

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

1970 • 253,849 citations

A Film Detection Method for Tritium‐Labelled Proteins and Nucleic Acids in Polyacrylamide Gels

1974 • 8,693 citations

Biosynthesis of lysosomal enzymes in fibroblasts. Synthesis as precursors of higher molecular weight.

1980 • 809 citations

Molecular cloning establishes proenkephalin as precursor of enkephalin-containing peptides

1982 • 621 citations

Eine Cerebrosidsulfatase aus Schweineniere

1964 • 278 citations

AB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2.

1978 • 274 citations

Gaucher's Disease: Deficiency of “cid”β-Glucosidase and Reconstitution of Enzyme Activity In Vitro

1971 • 257 citations

An activator stimulating the enzymic hydrolysis of sphingoglycolipids.

1976 • 159 citations

METACHROMATIC LEUKODYSTROPHY WITHOUT ARYLSULFATASE A DEFICIENCY

1979 • 119 citations

Purification and properties of a heat-stable glucocerebrosidase activating factor from control and Gaucher spleen.

1977 • 118 citations

Mechanism of activation of glucocerebrosidase by CO-β-glucosidase (glucosidase activator protein)

1981 • 115 citations

Maturation of alpha-L-iduronidase in cultured human fibroblasts.

1981 • 97 citations

A protein activator of galactosylceramide β-galactosidase

1982 • 86 citations

Immunological evidence for deficiency in an activator protein for sulfatide sulfatase in a variant form of metachromatic leukodystrophy.

1983 • 81 citations

Enhanced Breakdown of Arylsulfatase A in Multiple Sulfatase Deficiency

1982 • 76 citations

Biosynthesis of the sulfatide/GM1 activator protein (SAP-1) in control and mutant cultured skin fibroblasts

1986 • 73 citations

Niemann-Pick Disease, Type C: Evidence for the Deficiency of an Activating Factor Stimulating Sphingomyelin and Glucocerebroside Degradation

1980 • 72 citations

A variant form of metachromatic leukodystrophy without arylsulfatase deficiency

1982 • 66 citations

Biosynthesis and maturation of arylsulfatase B in normal and mutant cultured human fibroblasts.

1983 • 62 citations

The gene coding for a sphingolipid activator protein, SAP-1, is on human chromosome 10

1985 • 61 citations

Mapping of the gene coding for the human G_M2 activator protein to chromosome 5

1985 • 58 citations

Molecular Basis of Lysosomal Storage Disorders

1984 • 53 citations

Characterization of an activating factor required for hydrolysis of G_m2 ganglioside catalyzed by hexosaminidase A

1977 • 50 citations

Biochemical, immunological, and structural studies on a sphingolipid activator protein (SAP-1)

1984 • 47 citations

Assignment of the gene for human sphingolipid activator protein-2 (SAP-2) to chromosome 10.

1985 • 41 citations

Isolation of heat-stable glucocerebrosidase activators from the spleens of three variants of Gaucher's disease

1977 • 40 citations

Further studies on the activation of glucocerebrosidase by a heat-stable factor from Gaucher spleen

1985 • 35 citations

The cohydrolases in human spleen that stimulate glucosyl ceramide β-glucosidase

1983 • 34 citations

Studies on the activation of the enzymatic hydrolysis of sphingomyelin liposomes

1984 • 32 citations

Studies on a sphingolipid activator protein ( SAP-2) in fibroblasts from patients with lysosomal storage diseases, including Niemann-Pick disease Type C

1985 • 31 citations

Biosynthesis and maturation of alpha-N-acetylglucosaminidase in normal and Sanfilippo B-fibroblasts.

1984 • 20 citations

Evidence for the deficiency of ?-glucosidase-activating factor in fibroblasts of patients with I-cell disease

1982 • 10 citations