Hepatic protoporphyrin production in human protoporphyria

Metabolic Control and Disease.

1980 • 570 citations

Separation of erythrocytes according to age on a simplified density gradient.

1974 • 252 citations

Heme synthetase deficiency in human protoporphyria. Demonstration of the defect in liver and cultured skin fibroblasts.

1975 • 244 citations

Porphyrins in Human Diseases.

1977 • 225 citations

Repression of the Overproduction of Porphyrin Precursors in Acute Intermittent Porphyria by Intravenous Infusions of Hematin

1971 • 195 citations

Erythropoietic protoporphyria 10 years experience

1976 • 189 citations

In vivo lability of glucose-6-phosphate dehydrogenase in GdA- and Gdmediterranean deficiency

1968 • 184 citations

ACUTE INTERMITTENT PORPHYRIA: THE FIRST “OVERPRODUCTION DISEASE” LOCALIZED TO A SPECIFIC ENZYME

1965 • 183 citations

Diminished erythroid ferrochelatase activity in protoporphyria.

1975 • 161 citations

Erythropoietic protoporphyria and lead intoxication: the molecular basis for difference in cutaneous photosensitivity. I. Different rates of disappearance of protoporphyrin from the erythrocytes, both in vivo and in vitro.

1975 • 146 citations

Hepatic disease in erythropoietic protoporphyria

1975 • 127 citations

Factors affecting the excretion of porphyrin precursors by patients with acute intermittent porphyria I. The effect of diet

1964 • 121 citations

A Red Cell Enzyme Method for the Diagnosis of Acute Intermittent Porphyria

1974 • 120 citations

Principles of Internal Medicine

1966 • 108 citations

Hematin Therapy for Acute Porphyria

1979 • 108 citations

Effects of Hematin in Hepatic Porphyria

1975 • 106 citations

Direct spectrofluorometry of diluted erythrocytes and plasma: a rapid diagnostic method in primary and secondary porphyrinemias.

1976 • 101 citations

Erythropoietic protoporphyria: evidence for multiple sites of excess protoporphyrin formation

1971 • 98 citations

Erythropoietic protoporphyria

1963 • 91 citations

Hepatobiliary changes in erythropoietic protoporphyria.

1965 • 86 citations

Erythropoietic protoporphyria with features of a sideroblastic anaemia terminating in liver failure

1973 • 64 citations

INHERITANCE IN PROTOPORPHYRIA COMPARISON OF HÆM SYNTHETASE ACTIVITY IN SKIN FIBROBLASTS WITH CLINICAL FEATURES

1976 • 64 citations

Erythropoietic defects in protoporphyria: a study of factors involved in labelling of porphyrins and bile pigments from ALA- 3 H and glycine- 14 C.

1971 • 59 citations

HEMIN

1941 • 58 citations

ISOTOPE STUDIES ON A CASE OF ERYTHROPOIETIC PROTOPORPHYRIA.

1964 • 55 citations

`Erythropoietic' protoporphyria and cirrhosis in sisters

1973 • 48 citations

Liver Inclusions in Erythropoietic Protoporphyria

1975 • 45 citations

Enterohepatic Circulation and Conversion of Protoporphyrin to Bile Pigment in Man

1968 • 44 citations

Erythropoietic Protoporphyria

1965 • 37 citations

The origin of the increased protoporphyrin in erythrocytes of mice with experimentally induced porphyria.

1967 • 36 citations

Isotopic Studies of the Erythropoietic and Hepatic Components of Congenital Porphyria and ‘Erythropoietic’ Protoporphyria

1973 • 34 citations

Comparative Study of Protoporphyrins in Erythropoietic Protoporphyria and Griseofulvin-Induced Murine Protoporphyria

1977 • 32 citations

The "Glucose Effect" in Erythropoietic Protoporphyria

1968 • 32 citations

Erythropoietic protoporphyria: a family study.

1967 • 30 citations

Erythropoietic protoporphyria.

1976 • 28 citations

Erythropoietic Protoporphyria

1966 • 27 citations

Hepatic uptake of heme and hemopexin but not albumin

1974 • 25 citations

Hepatic and erythropoietic protoporphyria. Delta-aminolevulinic acid synthetase, fluorescence, and microfluorospectrophotometric study.

1971 • 24 citations

Erythropoietic protoporphyria. A light, electron, and polarization microscopical study of the liver in three patients.

1976 • 19 citations

Hematin administration to an adult with lead intoxication

1979 • 14 citations

The conversion of protoporphyrin-C14 to heme compounds and bilirubin in dogs

1966 • 14 citations

The Coexistence of Two Types of Porphyria in One Family

1978 • 10 citations

Rapid quantitative assay for erythrocyte porphyrins

1974 • 9 citations

Practical Clinical Hematology. Interpretations and Techniques.

1975 • 8 citations

Practical Clinical Hematology. Interpretations and Techniques

1974 • 7 citations

Hematin Clearance in Porphyria

2015 • 6 citations